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September 1991

Intraoperative Suprachoroidal Hemorrhage in Congenital Glaucoma Associated With Cutis Marmorata Telangiectatica Congenita

Author Affiliations

Petah-Tiqva, Israel

Arch Ophthalmol. 1991;109(9):1199-1200. doi:10.1001/archopht.1991.01080090023013

Cutis marmorata telangiectatica congenita (CMTC), first described by van Lohuizen,1 is characterized by congenital skin reticulated phlebectasia, which clinically improves with age. In 50% of affected patients, skin ulcerations, hemiatrophy, and cerebral vascular involvement were described.

Until recently, congenital glaucoma was described in association with CMTC in only four cases.2-4 We herein describe a boy exhibiting ipsilateral congenital glaucoma with skin telangiectasia and other features of this rare syndrome. During refiltering operation, nonexpulsive suprachoroidal hemorrhage developed, which can probably be linked to a choroidal vascular anomaly.

Report of a Case.  —A 6-year-old boy had been born with reticulated skin telangiectasia over the face, neck, and left side of his body. His motor development was delayed. Left buphthalmos, corneal edema, and high intraocular pressure were found at birth. Subsequently, he underwent trabeculotomy and since the intraocular pressure was still high, filtering operation was performed; he was unavailable for follow-up.

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