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July 1995

Juvenile Xanthogranuloma of the Corneoscleral Limbus

Author Affiliations

From the Department of Ophthalmology, Hahnemann University, Philadelphia, Pa (Dr Yanoff); Department of Ophthalmology, North Shore University Hospital, Manhasset, NY (Dr Perry); and Cornell University Medical College, New York, and Department of Ophthalmology, New York Eye and Ear Infirmary (Dr Perry).

Arch Ophthalmol. 1995;113(7):915-917. doi:10.1001/archopht.1995.01100070089030

Juvenile xanthogranuloma is a rare and usually benign skin disease of unknown cause that occurs in infants and young children. We studied a case of juvenile xanthogranuloma of the corneoscleral limbus in a 17-year-old black boy, who presented with a 5-month history of a lump in the right eye. The lesion extended from the superior limbus, fanning out as it proceeded posteriorly for 6 mm with a width of 9 mm and a height of 2 to 3 mm. This yellow-orange mass was vascular and firmly fixed to the underlying tissue. The lesion was diagnosed as a dermoid and observed for 7 months without documented growth before an uneventful excisional biopsy was performed. The pathologic diagnosis showed the characteristic picture of juvenile xanthogranuloma with numerous Touton giant cells. Lipid stains provided further confirmation.

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