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August 1997

Central Retinal Vein Occlusion in a Young Child With Cyanotic Heart Disease

Author Affiliations

Boston, Mass

Arch Ophthalmol. 1997;115(8):1077. doi:10.1001/archopht.1997.01100160247020

Central retinal vein occlusion (CRVO) is rarely reported in children. A young boy with cyanotic heart disease due to a double-outlet right ventricle, visceral heterotaxia, and asplenia syndrome required a bidirectional Glenn procedure1 (palliative cavopulmonary artery anastomosis) at age 5 months for treatment of the cardiac anomaly. Ischemic CRVO was noted at 20 months of age, with subsequent development of neovascular glaucoma.

Report of a Case.  A 20-month-old boy was initially examined because of mild right-sided weakness after a viral upper respiratory infection. Cranial computed tomography demonstrated multiple bilateral white matter lesions consistent with acute demyelinating encephalomyelitis. The workup included an ophthalmic examination.The right fundus showed engorged retinal veins with hemorrhages in every quadrant, multiple cotton-wool patches in the posterior pole, and macular edema. The disc was edematous. The left fundus was normal except for mild engorgement of the retinal veins. Two weeks after discovery of the CRVO,

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