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September 1997

Simple Choristoma of the Anterior Segment Containing Brain Tissue

Author Affiliations

From the Departments of Ophthalmology, British Columbia's Children's Hospital (Drs Marshman and Lyons), and University of British Columbia, Vancouver (Drs Marshman, Lyons, and White) and Victoria (Dr Young); and Department of Pathology, Vancouver Hospital and Health Sciences Centre, Vancouver (Dr White).

Arch Ophthalmol. 1997;115(9):1198-1200. doi:10.1001/archopht.1997.01100160368021

We report an unusual case of a simple choristoma of the anterior segment that contained only brain tissue. The clinical characteristics and findings of pathological examination of this unusual ocular malformation were reviewed. A newborn girl was seen with a fleshy, highly vascular cystic mass arising from the inferior limbus and extending across the cornea. On a computed tomographic scan, gross disruption of the anterior segment was present, with subluxation of the lens into the cyst. Excision of the abnormal tissue was followed by evisceration; polyglactin (Vicryl) ball implantation; patch graft of the globe; and, later, prosthetic fitting. Pathologic findings showed a choristomatous malformation, containing only mature brain tissue. To our knowledge, a choristoma in which the sole constituent is brain tissue has not previously been reported.

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