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Figure.  Association of Genetically Predicted Modifiable Risk Factors With Advanced Age-Related Macular Degeneration (AMD) and its Subtypes
Association of Genetically Predicted Modifiable Risk Factors With Advanced Age-Related Macular Degeneration (AMD) and its Subtypes

Odds ratios under the inverse-variance weighted mendelian randomization method are shown for a 1-SD increase in the logodds of ever having smoked regularly, 1-SD increase in the logodds of smoking cessation (former vs current smoking), 1-SD increase in the lifetime smoking index, 1-SD increase of the age at which an individual started smoking regularly, 1-SD increase of log-transformed alcoholic drinks per week, 1-SD increase in body mass index (calculated as 4.8 kg/m2); 10-mm Hg increase in systolic and diastolic pressure; 1-SD increase in the logodds of having type 2 diabetes; 1% increase in glycated hemoglobin (HbA1c); 18.02-mg/dL (to convert to mmol/L, multiply by 0.0555) increase in fasting glucose; and 1 log-transformed (pmol/L) increase in fasting insulin.

Table.  Details of the Summary-Level Data
Details of the Summary-Level Data
Supplement 1

eMethods. Study design, data sources, SNV selection, and statistical analysis

eTable 1. Smoking initiation exposure SNVs and their association with advanced AMD

eTable 2. Smoking cessation exposure SNVs and their association with advanced AMD

eTable 3. Lifetime smoking exposure SNVs and their association with advanced AMD

eTable 4. Age at smoking initiation exposure SNVs and their association with advanced AMD

eTable 5. Alcohol intake per week exposure SNVs and their association with advanced AMD

eTable 6. Body mass index exposure SNVs and their association with advanced AMD

eTable 7. Systolic blood pressure exposure SNVs and their association with advanced AMD

eTable 8. Diastolic blood pressure exposure SNVs and their association with advanced AMD

eTable 9. Type 2 diabetes exposure SNVs and their association with advanced AMD

eTable10. HbA1c exposure SNVs and their association with advanced AMD

eTable 11. Fasting glucose exposure SNVs and their association with advanced AMD

eTable 12. Fasting insulin exposure SNVs and their association with advanced AMD

eTable 13. Mendelian randomization analysis of modifiable risk factors for advanced AMD, geographic atrophy, and neovascular AMD

eFigure 1. Scatter plot of SNV-smoking initiation and SNV-AMD association estimates for the smoking initiation instrument

eFigure 2. Scatter plot of SNV-smoking cessation and SNV-AMD association estimates for the smoking cessation instrument

eFigure 3. Scatter plot of SNV-lifetime smoking and SNV-AMD association estimates for the lifetime smoking instrument

eFigure 4. Scatter plot of SNV-age at smoking initiation and SNV-AMD association estimates for the age at smoking initiation instrument

eFigure 5. Scatter plot of SNV-alcoholic drinks per week and SNV-AMD association estimates for the alcohol intake per week instrument

eFigure 6. Scatter plot of SNV-BMI and SNV-AMD association estimates for the body mass index instrument

eFigure 7. Scatter plot of SNV-systolic blood pressure and SNV-AMD association estimates for the systolic blood pressure instrument

eFigure 8. Scatter plot of SNV-diastolic blood pressure and SNV-AMD association estimates for the diastolic blood pressure instrument

eFigure 9. Scatter plot of SNV–type 2 diabetes and SNV-AMD association estimates for the type 2 diabetes instrument

eFigure 10. Scatter plot of SNV-HbA1c and SNV-AMD association estimates for the HbA1c instrument

eFigure 11. Scatter plot of SNV-fasting glucose and SNV-AMD association estimates for the fasting glucose instrument

eFigure12. Scatter plot of SNV-fasting insulin and SNV-AMD association estimates for the fasting insulin instrument

eReferences

1.
Li  JQ, Welchowski  T, Schmid  M, Mauschitz  MM, Holz  FG, Finger  RP.  Prevalence and incidence of age-related macular degeneration in Europe: a systematic review and meta-analysis.   Br J Ophthalmol. 2020;104(8):1077-1084. doi:10.1136/bjophthalmol-2019-314422PubMedGoogle ScholarCrossref
2.
Pennington  KL, DeAngelis  MM.  Epidemiology of age-related macular degeneration (AMD): associations with cardiovascular disease phenotypes and lipid factors.   Eye Vis (Lond). 2016;3:34. doi:10.1186/s40662-016-0063-5PubMedGoogle ScholarCrossref
3.
Mitchell  P, Liew  G, Gopinath  B, Wong  TY.  Age-related macular degeneration.   Lancet. 2018;392(10153):1147-1159. doi:10.1016/S0140-6736(18)31550-2PubMedGoogle ScholarCrossref
4.
Wong  WL, Su  X, Li  X,  et al.  Global prevalence of age-related macular degeneration and disease burden projection for 2020 and 2040: a systematic review and meta-analysis.   Lancet Glob Health. 2014;2(2):e106-e116. doi:10.1016/S2214-109X(13)70145-1PubMedGoogle ScholarCrossref
5.
Resnikoff  S, Pascolini  D, Etya’ale  D,  et al.  Global data on visual impairment in the year 2002.   Bull World Health Organ. 2004;82(11):844-851.PubMedGoogle Scholar
6.
Ferris  FL  III, Wilkinson  CP, Bird  A,  et al; Beckman Initiative for Macular Research Classification Committee.  Clinical classification of age-related macular degeneration.   Ophthalmology. 2013;120(4):844-851. doi:10.1016/j.ophtha.2012.10.036PubMedGoogle ScholarCrossref
7.
Finger  RP, Daien  V, Eldem  BM,  et al.  Anti-vascular endothelial growth factor in neovascular age-related macular degeneration—a systematic review of the impact of anti-VEGF on patient outcomes and healthcare systems.   BMC Ophthalmol. 2020;20(1):294. doi:10.1186/s12886-020-01554-2PubMedGoogle ScholarCrossref
8.
Rofagha  S, Bhisitkul  RB, Boyer  DS, Sadda  SR, Zhang  K; SEVEN-UP Study Group.  Seven-year outcomes in ranibizumab-treated patients in ANCHOR, MARINA, and HORIZON: a multicenter cohort study (SEVEN-UP).   Ophthalmology. 2013;120(11):2292-2299. doi:10.1016/j.ophtha.2013.03.046PubMedGoogle ScholarCrossref
9.
Lanzetta  P, Loewenstein  A; Vision Academy Steering Committee.  Fundamental principles of an anti-VEGF treatment regimen: optimal application of intravitreal anti-vascular endothelial growth factor therapy of macular diseases.   Graefes Arch Clin Exp Ophthalmol. 2017;255(7):1259-1273. doi:10.1007/s00417-017-3647-4PubMedGoogle ScholarCrossref
10.
Smith  W, Assink  J, Klein  R,  et al.  Risk factors for age-related macular degeneration: pooled findings from three continents.   Ophthalmology. 2001;108(4):697-704. doi:10.1016/S0161-6420(00)00580-7PubMedGoogle ScholarCrossref
11.
Mitchell  P, Wang  JJ, Smith  W, Leeder  SR.  Smoking and the 5-year incidence of age-related maculopathy: the Blue Mountains Eye Study.   Arch Ophthalmol. 2002;120(10):1357-1363. doi:10.1001/archopht.120.10.1357PubMedGoogle ScholarCrossref
12.
Lambert  NG, ElShelmani  H, Singh  MK,  et al.  Risk factors and biomarkers of age-related macular degeneration.   Prog Retin Eye Res. 2016;54:64-102. doi:10.1016/j.preteyeres.2016.04.003PubMedGoogle ScholarCrossref
13.
Adams  MK, Chong  EW, Williamson  E,  et al.  20/20—Alcohol and age-related macular degeneration: the Melbourne Collaborative Cohort Study.   Am J Epidemiol. 2012;176(4):289-298. doi:10.1093/aje/kws004PubMedGoogle ScholarCrossref
14.
Boekhoorn  SS, Vingerling  JR, Hofman  A, de Jong  PT.  Alcohol consumption and risk of aging macula disorder in a general population: the Rotterdam Study.   Arch Ophthalmol. 2008;126(6):834-839. doi:10.1001/archopht.126.6.834PubMedGoogle ScholarCrossref
15.
Fraser-Bell  S, Wu  J, Klein  R, Azen  SP, Varma  R.  Smoking, alcohol intake, estrogen use, and age-related macular degeneration in Latinos: the Los Angeles Latino Eye Study.   Am J Ophthalmol. 2006;141(1):79-87. doi:10.1016/j.ajo.2005.08.024PubMedGoogle ScholarCrossref
16.
Knudtson  MD, Klein  R, Klein  BE.  Alcohol consumption and the 15-year cumulative incidence of age-related macular degeneration.   Am J Ophthalmol. 2007;143(6):1026-1029. doi:10.1016/j.ajo.2007.01.036PubMedGoogle ScholarCrossref
17.
Zhang  QY, Tie  LJ, Wu  SS,  et al.  Overweight, obesity, and risk of age-related macular degeneration.   Invest Ophthalmol Vis Sci. 2016;57(3):1276-1283. doi:10.1167/iovs.15-18637PubMedGoogle ScholarCrossref
18.
Howard  KP, Klein  BE, Lee  KE, Klein  R.  Measures of body shape and adiposity as related to incidence of age-related eye diseases: observations from the Beaver Dam Eye Study.   Invest Ophthalmol Vis Sci. 2014;55(4):2592-2598. doi:10.1167/iovs.15-18637Google ScholarCrossref
19.
Chakravarthy  U, Wong  TY, Fletcher  A,  et al.  Clinical risk factors for age-related macular degeneration: a systematic review and meta-analysis.   BMC Ophthalmol. 2010;10:31. doi:10.1186/1471-2415-10-31PubMedGoogle ScholarCrossref
20.
Katsi  VK, Marketou  ME, Vrachatis  DA,  et al.  Essential hypertension in the pathogenesis of age-related macular degeneration: a review of the current evidence.   J Hypertens. 2015;33(12):2382-2388. doi:10.1097/HJH.0000000000000766PubMedGoogle ScholarCrossref
21.
Ghaem Maralani  H, Tai  BC, Wong  TY,  et al.  Metabolic syndrome and risk of age-related macular degeneration.   Retina. 2015;35(3):459-466. doi:10.1097/IAE.0000000000000338PubMedGoogle ScholarCrossref
22.
Cougnard-Grégoire  A, Delyfer  MN, Korobelnik  JF,  et al.  Long-term blood pressure and age-related macular degeneration: the ALIENOR study.   Invest Ophthalmol Vis Sci. 2013;54(3):1905-1912. doi:10.1167/iovs.12-10192PubMedGoogle ScholarCrossref
23.
Chakravarthy  U, Bailey  CC, Scanlon  PH,  et al.  Progression from early/intermediate to advanced forms of age-related macular degeneration in a large UK cohort: rates and risk factors.   Ophthalmol Retina. 2020;4(7):662-672. doi:10.1016/j.oret.2020.01.012PubMedGoogle ScholarCrossref
24.
Bikbov  MM, Zainullin  RM, Gilmanshin  TR,  et al.  Prevalence and associated factors of age-related macular degeneration in a Russian population: the Ural Eye and Medical Study.   Am J Ophthalmol. 2020;210:146-157. doi:10.1016/j.ajo.2019.10.004PubMedGoogle ScholarCrossref
25.
Chen  X, Rong  SS, Xu  Q,  et al.  Diabetes mellitus and risk of age-related macular degeneration: a systematic review and meta-analysis.   PLoS One. 2014;9(9):e108196. doi:10.1371/journal.pone.0108196PubMedGoogle Scholar
26.
Heesterbeek  TJ, Lorés-Motta  L, Hoyng  CB, Lechanteur  YTE, den Hollander  AI.  Risk factors for progression of age-related macular degeneration.   Ophthalmic Physiol Opt. 2020;40(2):140-170. doi:10.1111/opo.12675PubMedGoogle ScholarCrossref
27.
Colijn  JM, den Hollander  AI, Demirkan  A,  et al; European Eye Epidemiology Consortium; EYE-RISK Consortium.  Increased high-density lipoprotein levels associated with age-related macular degeneration: evidence from the EYE-RISK and European Eye Epidemiology Consortia.   Ophthalmology. 2019;126(3):393-406. doi:10.1016/j.ophtha.2018.09.045PubMedGoogle ScholarCrossref
28.
Age-Related Eye Disease Study Research Group.  A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8.   Arch Ophthalmol. 2001;119(10):1417-1436. doi:10.1001/archopht.119.10.1417PubMedGoogle ScholarCrossref
29.
Age-Related Eye Disease Study 2 Research Group.  Lutein + zeaxanthin and omega-3 fatty acids for age-related macular degeneration: the Age-Related Eye Disease Study 2 (AREDS2) randomized clinical trial.   JAMA. 2013;309(19):2005-2015. doi:10.1001/jama.2013.4997PubMedGoogle ScholarCrossref
30.
Chew  EY, Clemons  TE, Sangiovanni  JP,  et al; Age-Related Eye Disease Study 2 (AREDS2) Research Group.  Secondary analyses of the effects of lutein/zeaxanthin on age-related macular degeneration progression: AREDS2 report no. 3.   JAMA Ophthalmol. 2014;132(2):142-149. doi:10.1001/jamaophthalmol.2013.7376PubMedGoogle Scholar
31.
Smith  GD, Timpson  N, Ebrahim  S.  Strengthening causal inference in cardiovascular epidemiology through mendelian randomization.   Ann Med. 2008;40(7):524-541. doi:10.1080/07853890802010709PubMedGoogle ScholarCrossref
32.
Hingorani  A, Humphries  S.  Nature’s randomised trials.   Lancet. 2005;366(9501):1906-1908. doi:10.1016/S0140-6736(05)67767-7PubMedGoogle ScholarCrossref
33.
Burgess  S, Davey Smith  G.  Mendelian randomization implicates high-density lipoprotein cholesterol-associated mechanisms in etiology of age-related macular degeneration.   Ophthalmology. 2017;124(8):1165-1174. doi:10.1016/j.ophtha.2017.03.042PubMedGoogle ScholarCrossref
34.
Fan  Q, Maranville  JC, Fritsche  L,  et al.  HDL-cholesterol levels and risk of age-related macular degeneration: a multiethnic genetic study using mendelian randomization.   Int J Epidemiol. 2017;46(6):1891-1902. doi:10.1093/ije/dyx189PubMedGoogle ScholarCrossref
35.
Fritsche  LG, Igl  W, Bailey  JN,  et al.  A large genome-wide association study of age-related macular degeneration highlights contributions of rare and common variants.   Nat Genet. 2016;48(2):134-143. doi:10.1038/ng.3448PubMedGoogle ScholarCrossref
36.
Bowden  J, Davey Smith  G, Haycock  PC, Burgess  S.  Consistent estimation in mendelian randomization with some invalid instruments using a weighted median estimator.   Genet Epidemiol. 2016;40(4):304-314. doi:10.1002/gepi.21965PubMedGoogle ScholarCrossref
37.
Bowden  J, Davey Smith  G, Burgess  S.  Mendelian randomization with invalid instruments: effect estimation and bias detection through Egger regression.   Int J Epidemiol. 2015;44(2):512-525. doi:10.1093/ije/dyv080PubMedGoogle ScholarCrossref
38.
Verbanck  M, Chen  CY, Neale  B, Do  R.  Detection of widespread horizontal pleiotropy in causal relationships inferred from mendelian randomization between complex traits and diseases.   Nat Genet. 2018;50(5):693-698. doi:10.1038/s41588-018-0099-7PubMedGoogle ScholarCrossref
39.
Wootton  RE, Richmond  RC, Stuijfzand  BG,  et al.  Evidence for causal effects of lifetime smoking on risk for depression and schizophrenia: a mendelian randomisation study.   Psychol Med. 2020;50(14):2435-2443. doi:10.1017/S0033291719002678PubMedGoogle ScholarCrossref
40.
Bowden  J, Holmes  MV.  Meta-analysis and mendelian randomization: a review.   Res Synth Methods. 2019;10(4):486-496. Published online April 23, 2019. doi:10.1002/jrsm.1346PubMedGoogle ScholarCrossref
41.
Seddon  JM, Silver  RE, Kwong  M, Rosner  B.  Risk prediction for progression of macular degeneration: 10 common and rare genetic variants, demographic, environmental, and macular covariates.   Invest Ophthalmol Vis Sci. 2015;56(4):2192-2202. doi:10.1167/iovs.14-15841PubMedGoogle ScholarCrossref
42.
Wang  JJ, Rochtchina  E, Smith  W,  et al.  Combined effects of complement factor H genotypes, fish consumption, and inflammatory markers on long-term risk for age-related macular degeneration in a cohort.   Am J Epidemiol. 2009;169(5):633-641. doi:10.1093/aje/kwn358PubMedGoogle ScholarCrossref
43.
Jonasson  F, Fisher  DE, Eiriksdottir  G,  et al.  Five-year incidence, progression, and risk factors for age-related macular degeneration: the age, gene/environment susceptibility study.   Ophthalmology. 2014;121(9):1766-1772. doi:10.1016/j.ophtha.2014.03.013PubMedGoogle ScholarCrossref
44.
Vingerling  JR, Hofman  A, Grobbee  DE, de Jong  PT.  Age-related macular degeneration and smoking. the Rotterdam Study.   Arch Ophthalmol. 1996;114(10):1193-1196. doi:10.1001/archopht.1996.01100140393005PubMedGoogle ScholarCrossref
45.
Khandhadia  S, Lotery  A.  Oxidation and age-related macular degeneration: insights from molecular biology.   Expert Rev Mol Med. 2010;12:e34. doi:10.1017/S146239941000164XPubMedGoogle Scholar
46.
Alberg  A.  The influence of cigarette smoking on circulating concentrations of antioxidant micronutrients.   Toxicology. 2002;180(2):121-137. doi:10.1016/S0300-483X(02)00386-4PubMedGoogle ScholarCrossref
47.
Chang  MA, Bressler  SB, Munoz  B, West  SK.  Racial differences and other risk factors for incidence and progression of age-related macular degeneration: Salisbury Eye Evaluation (SEE) project.   Invest Ophthalmol Vis Sci. 2008;49(6):2395-2402. doi:10.1167/iovs.07-1584PubMedGoogle ScholarCrossref
48.
Khan  JC, Thurlby  DA, Shahid  H,  et al; Genetic Factors in AMD Study.  Smoking and age related macular degeneration: the number of pack years of cigarette smoking is a major determinant of risk for both geographic atrophy and choroidal neovascularisation.   Br J Ophthalmol. 2006;90(1):75-80. doi:10.1136/bjo.2005.073643PubMedGoogle ScholarCrossref
49.
Thornton  J, Edwards  R, Mitchell  P, Harrison  RA, Buchan  I, Kelly  SP.  Smoking and age-related macular degeneration: a review of association.   Eye (Lond). 2005;19(9):935-944. doi:10.1038/sj.eye.6701978PubMedGoogle ScholarCrossref
50.
Ciulla  TA, Harris  A, Martin  BJ.  Ocular perfusion and age-related macular degeneration.   Acta Ophthalmol Scand. 2001;79(2):108-115. doi:10.1034/j.1600-0420.2001.079002108.xPubMedGoogle ScholarCrossref
51.
Suñer  IJ, Espinosa-Heidmann  DG, Marin-Castano  ME, Hernandez  EP, Pereira-Simon  S, Cousins  SW.  Nicotine increases size and severity of experimental choroidal neovascularization.   Invest Ophthalmol Vis Sci. 2004;45(1):311-317. doi:10.1167/iovs.03-0733PubMedGoogle ScholarCrossref
52.
Akishima  S, Matsushita  S, Sato  F,  et al.  Cigarette-smoke-induced vasoconstriction of peripheral arteries: evaluation by synchrotron radiation microangiography.   Circ J. 2007;71(3):418-422. doi:10.1253/circj.71.418PubMedGoogle ScholarCrossref
53.
Aiello  LP, Northrup  JM, Keyt  BA, Takagi  H, Iwamoto  MA.  Hypoxic regulation of vascular endothelial growth factor in retinal cells.   Arch Ophthalmol. 1995;113(12):1538-1544. doi:10.1001/archopht.1995.01100120068012PubMedGoogle ScholarCrossref
54.
Kunchithapautham  K, Atkinson  C, Rohrer  B.  Smoke exposure causes endoplasmic reticulum stress and lipid accumulation in retinal pigment epithelium through oxidative stress and complement activation.   J Biol Chem. 2014;289(21):14534-14546. doi:10.1074/jbc.M114.564674PubMedGoogle ScholarCrossref
55.
Wang  L, Kondo  N, Cano  M,  et al.  Nrf2 signaling modulates cigarette smoke-induced complement activation in retinal pigmented epithelial cells.   Free Radic Biol Med. 2014;70:155-166. doi:10.1016/j.freeradbiomed.2014.01.015PubMedGoogle ScholarCrossref
56.
Gibson  J, Hakobyan  S, Cree  AJ,  et al.  Variation in complement component C1 inhibitor in age-related macular degeneration.   Immunobiology. 2012;217(2):251-255. doi:10.1016/j.imbio.2011.07.015PubMedGoogle ScholarCrossref
57.
Bird  AC.  Therapeutic targets in age-related macular disease.   J Clin Invest. 2010;120(9):3033-3041. doi:10.1172/JCI42437PubMedGoogle ScholarCrossref
58.
Ambati  J, Atkinson  JP, Gelfand  BD.  Immunology of age-related macular degeneration.   Nat Rev Immunol. 2013;13(6):438-451. doi:10.1038/nri3459PubMedGoogle ScholarCrossref
59.
Chong  EW, Kreis  AJ, Wong  TY, Simpson  JA, Guymer  RH.  Alcohol consumption and the risk of age-related macular degeneration: a systematic review and meta-analysis.   Am J Ophthalmol. 2008;145(4):707-715. doi:10.1016/j.ajo.2007.12.005PubMedGoogle ScholarCrossref
60.
Dinu  M, Pagliai  G, Casini  A, Sofi  F.  Food groups and risk of age-related macular degeneration: a systematic review with meta-analysis.   Eur J Nutr. 2019;58(5):2123-2143. doi:10.1007/s00394-018-1771-5PubMedGoogle ScholarCrossref
61.
Obisesan  TO, Hirsch  R, Kosoko  O, Carlson  L, Parrott  M.  Moderate wine consumption is associated with decreased odds of developing age-related macular degeneration in NHANES-1.   J Am Geriatr Soc. 1998;46(1):1-7. doi:10.1111/j.1532-5415.1998.tb01005.xPubMedGoogle ScholarCrossref
62.
Das  SK, Vasudevan  DM.  Alcohol-induced oxidative stress.   Life Sci. 2007;81(3):177-187. doi:10.1016/j.lfs.2007.05.005PubMedGoogle ScholarCrossref
63.
Cederbaum  AI.  Role of lipid peroxidation and oxidative stress in alcohol toxicity .  Free Radic Biol Med. 1989;7(5):537-539. doi:10.1016/0891-5849(89)90029-4PubMedGoogle ScholarCrossref
64.
Klein  R, Myers  CE, Klein  BE.  Vasodilators, blood pressure-lowering medications, and age-related macular degeneration: the Beaver Dam Eye Study.   Ophthalmology. 2014;121(8):1604-1611. doi:10.1016/j.ophtha.2014.03.005PubMedGoogle ScholarCrossref
65.
Cummings  M, Cunha-Vaz  J.  Treatment of neovascular age-related macular degeneration in patients with diabetes.   Clin Ophthalmol. 2008;2(2):369-375. doi:10.2147/OPTH.S2560PubMedGoogle Scholar
66.
Sander  B, Larsen  M, Moldow  B, Lund-Andersen  H.  Diabetic macular edema: passive and active transport of fluorescein through the blood-retina barrier.   Invest Ophthalmol Vis Sci. 2001;42(2):433-438.PubMedGoogle Scholar
67.
Burgess  S, Scott  RA, Timpson  NJ, Davey Smith  G, Thompson  SG; EPIC- InterAct Consortium.  Using published data in mendelian randomization: a blueprint for efficient identification of causal risk factors.   Eur J Epidemiol. 2015;30(7):543-552. doi:10.1007/s10654-015-0011-zPubMedGoogle ScholarCrossref
68.
Lawlor  DA.  Commentary: two-sample mendelian randomization: opportunities and challenges.   Int J Epidemiol. 2016;45(3):908-915. doi:10.1093/ije/dyw127PubMedGoogle ScholarCrossref
69.
Burgess  S, Davey Smith  G, Davies  NM,  et al.  Guidelines for performing mendelian randomization investigations.   Wellcome Open Res. 2020;4:186. doi:10.12688/wellcomeopenres.15555.2PubMedGoogle ScholarCrossref
70.
Didelez  V, Sheehan  N.  Mendelian randomization as an instrumental variable approach to causal inference.   Stat Methods Med Res. 2007;16(4):309-330. doi:10.1177/0962280206077743PubMedGoogle ScholarCrossref
71.
VanderWeele  TJ, Tchetgen Tchetgen  EJ, Cornelis  M, Kraft  P.  Methodological challenges in mendelian randomization.   Epidemiology. 2014;25(3):427-435. doi:10.1097/EDE.0000000000000081PubMedGoogle ScholarCrossref
72.
Davies  NM, Holmes  MV, Davey Smith  G.  Reading mendelian randomisation studies: a guide, glossary, and checklist for clinicians.   BMJ. 2018;362:k601. doi:10.1136/bmj.k601PubMedGoogle Scholar
73.
Burgess  S, Bowden  J, Fall  T, Ingelsson  E, Thompson  SG.  Sensitivity analyses for robust causal inference from mendelian randomization analyses with multiple genetic variants.   Epidemiology. 2017;28(1):30-42. doi:10.1097/EDE.0000000000000559PubMedGoogle ScholarCrossref
74.
Slob  EAW, Burgess  S.  A comparison of robust mendelian randomization methods using summary data.   Genet Epidemiol. 2020;44(4):313-329. doi:10.1002/gepi.22295PubMedGoogle ScholarCrossref
Original Investigation
November 4, 2021

Association of Smoking, Alcohol Consumption, Blood Pressure, Body Mass Index, and Glycemic Risk Factors With Age-Related Macular Degeneration: A Mendelian Randomization Study

Author Affiliations
  • 1Institute of Health Informatics, University College London, London, United Kingdom
  • 2Health Data Research UK London, University College London, London, United Kingdom
  • 3University College London British Heart Foundation Research Accelerator, London, United Kingdom
  • 4Institute of Cardiovascular Science, University College London, London, United Kingdom
  • 5Moorfields Eye Hospital, London, United Kingdom
  • 6UCL Institute of Ophthalmology, University College London, London, United Kingdom
  • 7Clinical Pharmacology, William Harvey Research Institute, Queen Mary University of London, London, United Kingdom
  • 8UCL Genetics Institute, University College London, London, United Kingdom
  • 9Department of Public Health and Primary Care, University of Cambridge, Cambridge, United Kingdom
  • 10MRC Biostatistics Unit, University of Cambridge, Cambridge, United Kingdom
JAMA Ophthalmol. 2021;139(12):1299-1306. doi:10.1001/jamaophthalmol.2021.4601
Key Points

Question  Are smoking, alcohol intake, blood pressure, body mass index, and glycemic traits associated with age-related macular degeneration (AMD)?

Findings  In this mendelian randomization study, genetically predicted smoking initiation and lifetime smoking were associated with elevated risk of advanced AMD, genetically predicted smoking cessation was associated with decreased risk of advanced AMD, and genetically predicted alcohol intake was associated with increased risk of geographic atrophy.

Meaning  These findings support a potential causal association of alcohol consumption with an increased risk of geographic atrophy, smoking initiation and lifetime smoking with an increased risk of advanced AMD, and smoking cessation with a decreased risk of advanced AMD.

Abstract

Importance  Advanced age-related macular degeneration (AMD) is a leading cause of blindness in Western countries. Causal, modifiable risk factors need to be identified to develop preventive measures for advanced AMD.

Objective  To assess whether smoking, alcohol consumption, blood pressure, body mass index, and glycemic traits are associated with increased risk of advanced AMD.

Design, Setting, Participants  This study used 2-sample mendelian randomization. Genetic instruments composed of variants associated with risk factors at genome-wide significance (P < 5 × 10−8) were obtained from published genome-wide association studies. Summary-level statistics for these instruments were obtained for advanced AMD from the International AMD Genomics Consortium 2016 data set, which consisted of 16 144 individuals with AMD and 17 832 control individuals. Data were analyzed from July 2020 to September 2021.

Exposures  Smoking initiation, smoking cessation, lifetime smoking, age at smoking initiation, alcoholic drinks per week, body mass index, systolic and diastolic blood pressure, type 2 diabetes, glycated hemoglobin, fasting glucose, and fasting insulin.

Main Outcomes and Measures  Advanced AMD and its subtypes, geographic atrophy (GA), and neovascular AMD.

Results  A 1-SD increase in logodds of genetically predicted smoking initiation was associated with higher risk of advanced AMD (odds ratio [OR], 1.26; 95% CI, 1.13-1.40; P < .001), while a 1-SD increase in logodds of genetically predicted smoking cessation (former vs current smoking) was associated with lower risk of advanced AMD (OR, 0.66; 95% CI, 0.50-0.87; P = .003). Genetically predicted increased lifetime smoking was associated with increased risk of advanced AMD (OR per 1-SD increase in lifetime smoking behavior, 1.32; 95% CI, 1.09-1.59; P = .004). Genetically predicted alcohol consumption was associated with higher risk of GA (OR per 1-SD increase of log-transformed alcoholic drinks per week, 2.70; 95% CI, 1.48-4.94; P = .001). There was insufficient evidence to suggest that genetically predicted blood pressure, body mass index, and glycemic traits were associated with advanced AMD.

Conclusions and Relevance  This study provides genetic evidence that increased alcohol intake may be a causal risk factor for GA. As there are currently no known treatments for GA, this finding has important public health implications. These results also support previous observational studies associating smoking behavior with risk of advanced AMD, thus reinforcing existing public health messages regarding the risk of blindness associated with smoking.

Introduction

Age-related macular degeneration (AMD) is a leading cause of blindness in Western countries,1-4 accounting for 8.7% of blindness worldwide.5 The prevalence of AMD is projected to increase by 47% in the next 20 years because of population aging, posing a major burden to health care systems across the world.4 Advanced AMD consists of geographic atrophy (GA) and neovascular AMD (nAMD).6 Treatment is currently only available for nAMD and comes in the form of intravitreal injections of anti–vascular endothelial growth factor.3 This treatment is invasive, expensive, of limited effectiveness, and poses a considerable burden on patients.7-9 Therefore, increased public health efforts need to be directed toward prevention of advanced AMD. Identifying causal, modifiable risk factors for advanced AMD is critical to implementing interventions for prevention.

Observational epidemiological studies have investigated the associations of lifestyle and metabolic risk factors (smoking,10-12 alcohol consumption,13-16 obesity,8,17-19 blood pressure,20-22 glycemic traits,21,23-25 and dyslipidemia2,26,27) with AMD, but the findings are inconsistent and cannot be established as causal owing to limitations introduced by confounding and reverse causality. Randomized clinical trials (RCTs) allow reliable causal inferences to be drawn and have shown that dietary intake of specific high-dose combinations of zinc and antioxidants reduces progression from intermediate to advanced AMD.28-30 However, for diseases of aging, such as AMD, where there may be a long lag time between exposure to risk factors and clinical manifestation of disease, RCTs may be prohibitively expensive, time consuming, and infeasible, particularly for exposures such as smoking, alcohol intake, obesity, hypertension, glycemic traits, and blood lipid levels.

Quiz Ref IDMendelian randomization (MR) is a technique that has been used to assess potential causal associations across a wide range of diseases. MR is based on the principle that if a genetic variant causes a change in an exposure (eg, smoking or alcohol intake), and if this exposure is causal for a disease (eg, advanced AMD), then the genetic variant should also be associated with risk of the disease. This method exploits the random allocation of genetic variants at meiosis,31 rendering MR studies similar to RCTs in that they are less prone to confounding than classical observational epidemiological studies. MR studies also mitigate the problem of reverse causation because the genotype is invariant and not modified by disease.32 MR techniques based on multiple genetic variants selected from across the genome have found a causal role for increased levels of high-density lipoprotein cholesterol, but not low-density lipoprotein cholesterol or triglycerides, in advanced AMD risk.33,34

Here we use MR to assess the potential causal role of other exposures that are amenable to intervention (ie, smoking, alcohol intake, body mass index [BMI], blood pressure, and glycemic traits) on the risk of advanced AMD and its subtypes, GA and nAMD, using publicly available data.

Methods
Study Design

Two-sample MR was performed, whereby summary-level data of genetic variants associated with smoking initiation (ever having smoked regularly), smoking cessation (former vs current smoking), lifetime smoking (represented by an index which captures smoking status, duration, heaviness, and cessation), age at smoking initiation, weekly alcohol intake, BMI, systolic and diastolic blood pressure, type 2 diabetes, glycated hemoglobin (HbA1c), fasting glucose level, and fasting insulin level were obtained from study samples that did not overlap with those for advanced AMD and its subtypes (eMethods in Supplement 1). Ethical approval for each data set had been obtained in the original studies.

Data Sources

Summary-level statistics for smoking traits, alcohol intake, BMI, blood pressure, and glycemic traits were obtained from, to our knowledge, the largest genome-wide association studies (GWAS) for these exposures to date (eMethods in Supplement 1). Summary-level genetic association data for advanced AMD, GA, and nAMD were obtained from the International AMD Genomics Consortium (IAMDGC) 2016 data set.35 Data were analyzed from July 2020 to September 2021. The number of participants in each study, the race and ethnicity of the participants, and the number of single-nucleotide variants (SNVs; formerly SNPs) in the genetic instruments for each exposure are provided in the Table. The SNVs used as instrumental variables for the exposures in this study (eTables 1-12 in Supplement 1) were obtained from the studies listed in the Table. SNVs were selected according to criteria outlined in the eMethods in Supplement 1.

Statistical Analysis

We performed univariable inverse-variance–weighted (IVW) 2-sample MR analyses under a multiplicative random-effects model to examine the potential causal associations of smoking, alcohol intake, BMI, blood pressure, and glycemic risk factors with the risk of advanced AMD and its subtypes, GA and nAMD (eMethods in Supplement 1).

Additionally, we conducted sensitivity analyses using the weighted median,36 MR-Egger,37 and MR pleiotropy residual sum and outlier (MR-PRESSO)38 methods, as well as multivariable MR (MVMR) with smoking traits adjusted for alcohol intake and vice versa (eMethods in Supplement 1).

We analyzed 12 potentially modifiable lifestyle and metabolic exposures (Table). Wald test was used to calculate 2-tailed P values. Using a conservative approach, we applied a Bonferroni-corrected significance level of .004 (.05 divided by 12). Analyses were conducted using the MR, MR-PRESSO, and 2-sample MR packages in R version 3.5.0 (the R Foundation).

Results
Association of Smoking With Risk of Advanced AMD

Quiz Ref IDGenetic predisposition to smoking initiation was associated with overall risk of advanced AMD under the IVW method (OR [odds ratio], 1.26; 95% CI, 1.13-1.40; P < .001) (Figure; eFigure 1 and eTable 13 in Supplement 1). This was supported by the MVMR analysis (OR, 1.19; 95% CI, 1.05-1.36; P = .007) and weighted median analysis (OR, 1.20; 95% CI, 1.02-1.40; P = .03) (Figure; eFigure 1 and eTable 13 in Supplement 1). The results were similar for nAMD (IVW: OR, 1.26; 95% CI, 1.11-1.43; P < .001; MVMR: OR, 1.18; 95% CI, 1.02-1.37; P = .02; weighted median: OR, 1.29; 95% CI, 1.08-1.54; P = .005). Smoking initiation was not associated with GA (IVW: OR, 1.24; 95% CI, 1.03-1.49; P = .02; weighted median: OR, 1.31; 95% CI, 1.00-1.72; P = .05) (Figure; eTable 13 in Supplement 1). There was no indication of heterogeneity using the Cochran Q statistic (Figure) or directional pleiotropy using MR-Egger and MR-PRESSO methods (eTable 13 in Supplement 1).

Genetically predicted smoking cessation was protective for advanced AMD compared with persistent smoking (IVW: OR, 0.66; 95% CI, 0.50-0.87; P = .003; MVMR: OR, 0.71; 95% CI, 0.57-0.88; P = .002; MR-Egger: OR, 0.43; 95% CI, 0.21-0.87; P = .02) (Figure; eFigure 2 and eTable 13 in Supplement 1). There was no association between smoking cessation and nAMD or GA (Figure; eTable 13 in Supplement 1). No evidence was found of heterogeneity using the Cochran Q statistic (Figure) or directional pleiotropy using MR-Egger and MR-PRESSO (eTable 13 in Supplement 1).

Genetically predicted lifetime smoking (represented by a composite index taking into account smoking status, duration, heaviness, and cessation)39 was associated with higher odds of advanced AMD (IVW: OR, 1.32; 95% CI, 1.09-1.59; P = .004; MVMR: OR, 1.48; 95% CI, 1.14-1.94; P = .004; weighted median: OR, 1.42; 95% CI, 1.11-1.81; P = .005) (Figure; eFigure 3 and eTable 13 in Supplement 1). The results were similar for nAMD (IVW: OR, 1.41; 95% CI, 1.14-1.74; P = .001; MVMR: OR, 1.62; 95% CI, 1.19-2.19; P = .002; weighted median: OR, 1.42; 95% CI, 1.08-1.88; P = .01) (Figure; eTable 13 in Supplement 1). The association with GA was not statistically significant. Heterogeneity was detected in the variant-specific estimates for lifetime smoking (Figure). However, the multiplicative random-effects IVW method accounts for heterogeneity and provides valid estimates under the assumption of balanced pleiotropy.40 There was no indication of directional (unbalanced) pleiotropy using the MR-Egger method. The MR-PRESSO test detected no outliers for advanced AMD or nAMD and 1 outlier for GA, with no significant difference in the estimates before and after adjusting for the outlier (eTable 13 in Supplement 1). The age at which smoking was initiated was not found to be associated with risk of advanced AMD and its subtypes (Figure; eFigure 4 and eTable 13 in Supplement 1).

Association of Alcohol Consumption With Risk of Advanced AMD

We found no association between increased genetically predicted alcohol consumption and risk of advanced AMD using IVW (OR, 1.57; 95% CI, 1.03-2.40; P = .04), MVMR (OR, 1.65; 95% CI, 1.21-2.26; P = .002), weighted median (OR, 2.04; 95% CI, 1.23-3.39; P = .006), or MR-PRESSO (OR, 1.47; 95% CI, 1.02-2.10; P = .04) (Figure; eFigure 5 and eTable 13 in Supplement 1). Examination of advanced AMD subtypes showed a strong association between higher alcohol intake and GA (IVW: OR, 2.70; 95% CI, 1.48-4.94; P = .001; MVMR: OR, 2.83; 95% CI, 1.64-4.88; P < .001; and MR-PRESSO: OR, 2.50; 95% CI, 1.42-4.42; P = .002), but not nAMD (Figure; eTable 13 in Supplement 1). There was evidence of heterogeneity (Figure), but this was accounted for under the multiplicative random-effects IVW method.40 There was no indication of directional (unbalanced) pleiotropy using MR-Egger. The MR-PRESSO test detected 3 outliers for advanced AMD—1 for GA and 2 for nAMD—but there was no significant difference between the estimates before and after correction for outliers (eTable 13 in Supplement 1).

Association of BMI, Blood Pressure, and Glycemic Risk Factors With Risk of Advanced AMD

There was no evidence that BMI, blood pressure, type 2 diabetes, HbA1c, fasting glucose level, or fasting insulin level had a causal association with the risk of AMD using MR (Figure; eFigures 6-12 and eTable 13 in Supplement 1).

Discussion
Main Findings

Quiz Ref IDThis study used an MR framework to explore potential causal associations between the risk of advanced AMD and the following modifiable risk factors: smoking, alcohol consumption, BMI, blood pressure, and glycemic traits. We found genetic evidence supporting a potential causal association between smoking initiation and advanced AMD risk consistent with previous observational studies. This association was stronger for nAMD than for GA. Similar results were found for lifetime smoking behavior. Additionally, smoking cessation was associated with a decreased risk of advanced AMD, specifically nAMD, compared with persistent smoking. We also found suggestive evidence for a possible causal association between increased alcohol consumption and risk of advanced AMD that was likely driven by a strong association with GA. There was insufficient evidence to suggest a potential causal association with the other exposures, namely BMI, blood pressure, or glycemic risk factors, on advanced AMD risk.

Results in Context With the Published Literature

Conventional observational studies have consistently implicated smoking as a risk factor for developing AMD (OR, 1.7-4.6),10,11,41-43 with 1 study reporting the risk of AMD reduced to baseline 20 years after smoking cessation.44 Using MR techniques, we found genetic evidence to support that smoking initiation and lifetime smoking behavior may be causally associated with risk of advanced AMD and that smoking cessation is protective. Several theories have been proposed to explain the association between smoking and AMD. Oxidative stress is thought to play a major role in AMD pathogenesis.45 Smoking is known to decrease levels of antioxidants,46 resulting in the disruption of the retinal pigment epithelium barrier and leading to the formation of drusen and neovascularization.47-50 Smoking can also upregulate endothelial smooth muscle cell proliferation, leading to choroidal neovascularization.51 Atherosclerosis or vasoconstriction secondary to smoking could cause hypoxic conditions in the retina,52 stimulating production of vascular endothelial growth factor and resulting in retinal endothelial cell proliferation and neovascularization.53 Smoking has also been found to be associated with the production of inflammatory mediators and activation of the complement cascade involved in the pathogenesis of AMD.54-56 While these hypotheses may explain how smoking can cause AMD generally, it has been unclear whether and how smoking affects GA and nAMD differently. Our finding that smoking behavior has a greater potential association with nAMD compared with GA may be a reflection of how the pathogenesis of nAMD diverges from what is assumed to be the underlying default pathway of early AMD to GA.57,58 Further investigation is required to provide insights into how these pathways differ.

The evidence in the literature for an association between alcohol consumption and AMD risk is less robust than for smoking. While high alcohol intake has been reported to be associated with an increased risk of AMD, a systematic review concluded that residual confounding effects from smoking could not be ruled out.13,59,60 One study has conversely reported a protective effect with moderate alcohol consumption.61 Our results provide genetic evidence of a potential causal association between increased weekly alcohol consumption and risk of GA. While there are no studies, to our knowledge, looking at the role of alcohol consumption in the pathophysiology of GA specifically, the mechanism of alcohol as a risk factor for AMD is thought to be related to oxidative damage. Alcohol depletes antioxidant levels and results in the production of reactive oxygen species.62,63 Further studies are required to investigate why increased alcohol intake appears to have a causal association with GA but not with nAMD.

The effects of BMI and blood pressure on AMD are uncertain. Some observational studies have found increased BMI and blood pressure to be associated with increased AMD risk, whereas others showed no association.17,26 A meta-analysis of cohort studies found an increased risk of advanced AMD in individuals with obesity.17 One cohort study found antihypertensive medication to be associated with increased AMD risk.64 However, cohort studies are prone to confounding, and meta-analyses are prone to publication bias. Our MR estimates did not indicate potential causal associations for either BMI or blood pressure traits with risk of advanced AMD.

Reports on the association between diabetes and AMD are conflicting. A recent meta-analysis found that diabetes was associated with increased risk of AMD.25 However, the authors stated that it was not possible to rule out underlying confounders, as most of the included studies only adjusted for age and sex. Other studies have reported a protective effect for diabetic retinopathy on AMD risk.65 While both AMD and diabetic retinopathy are inflammatory retinal conditions, AMD is characterized by alterations in the outer blood-retinal barrier (BRB) and diabetic retinopathy by changes in the inner BRB. Damage to the inner BRB in diabetes is associated with upregulation of outer BRB activity,66 which could potentially provide a protective mechanism for AMD. The MR estimates for the 4 glycemic traits analyzed in this study did not reach statistical significance.

Implications for Clinical Practice and Health Policy

This study provides genetic evidence that smoking initiation and lifetime smoking behavior are potential causal risk factors for advanced AMD, and that stopping smoking may be protective against the risk of advanced AMD. The detrimental effects of smoking on multiple conditions, such as cardiovascular disease, cancers, and chronic obstructive pulmonary disease, are well known. Public health campaigns should disseminate information that smoking can also lead to blindness as an additional deterrent against smoking. We also found genetic evidence that increased alcohol consumption has a potential causal association with GA risk. Here again, public health messages and clinical advice regarding the harms of excessive alcohol intake should include the risk of blindness, especially given that there are currently no effective treatments for GA. Given the deterioration in quality of life and the cost to health and social care systems of managing advanced AMD, increased funding should be allocated to smoking cessation and alcohol reduction programs to minimize the health burden of advanced AMD.

Strengths and Limitations

This study has several strengths. The use of MR mitigates bias from reverse causation and confounding that can affect findings from observational studies. The 2-sample MR approach increases statistical power as it allows independent large GWAS summary data sets to be used for both exposures and outcomes.67,68 The use of multiple genetic variants as instruments for each of the risk factors enables SNVs across the whole genome to be used to assess the association of each of the modifiable exposures with risk of advanced AMD. This allowed us to perform sensitivity analyses to detect and correct for directional pleiotropy. Most of the participants in the GWAS data sets were of European descent, thus minimizing bias due to population stratification.

Quiz Ref IDThis study also has several limitations. While we used summary statistics from the largest known advanced AMD GWAS to date, the number of advanced AMD cases, especially for GA, was still relatively small compared with other outcomes used in MR studies, such as cardiovascular disease. This might have resulted in insufficient statistical power to detect associations with some of the exposures analyzed. Additionally, effect sizes from MR analyses should be interpreted with caution. This is because the MR estimate is better interpreted as a test statistic for a causal hypothesis rather than the expected impact of a clinical intervention at a specific point in time.69-71 Another potential limitation in MR analyses is directional horizontal pleiotropy, which can occur if genetic variants affect advanced AMD independently of the risk factors investigated. To identify and adjust for pleiotropy, we performed sensitivity analyses using MR-Egger, weighted median, MVMR, and MR-PRESSO methods (eFigures 1-12 in Supplement 1). These tests can provide reliable inferences when some genetic variants are pleiotropic.72-74 There was no evidence for directional pleiotropy using these tests. However, it is not possible to completely rule out the presence of residual pleiotropy. Additionally, we were unable to test the nonlinear association for nonbinary exposures, such as alcohol consumption, blood pressure, BMI, and quantitative glycemic traits, with advanced AMD risk, as MR analysis assumes a linear association between exposure and outcome.

Conclusions

We found genetic evidence that increased alcohol consumption has a potential causal association with risk of GA. We also present genetic evidence that smoking initiation and lifetime smoking behavior may be casually associated with risk of advanced AMD, while smoking cessation results in a lower risk of advanced AMD than persistent smoking. These associations were stronger for nAMD than for GA. To reduce the prevalence of advanced AMD in aging populations, public health campaigns and programs to support smoking abstention, smoking cessation, and reduced alcohol intake should incorporate the evidence that these activities can lead to blindness. The finding that smoking and alcohol have differential effects on nAMD and GA may prompt future studies examining the different pathologies of these 2 forms of advanced AMD.

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Article Information

Accepted for Publication: September 20, 2021.

Published Online: November 4, 2021. doi:10.1001/jamaophthalmol.2021.4601

Open Access: This is an open access article distributed under the terms of the CC-BY License. © 2021 Kuan V et al. JAMA Ophthalmology.

Corresponding Author: Valerie Kuan, PhD, Institute of Health Informatics, University College London, 222 Euston Rd, London NW1 2DA, United Kingdom (v.kuan@ucl.ac.uk).

Author Contributions: Dr Kuan had full access to all of the data in the study and takes responsibility for the integrity of the data and the accuracy of the data analysis.

Concept and design: Kuan, Hingorani, Tufail, Sofat.

Acquisition, analysis, or interpretation of data: Kuan, Warwick, Tufail, Cipriani, Burgess, Sofat.

Drafting of the manuscript: Kuan, Warwick.

Critical revision of the manuscript for important intellectual content: Kuan, Hingorani, Tufail, Cipriani, Burgess, Sofat.

Statistical analysis: Kuan, Warwick, Cipriani, Burgess.

Obtained funding: Cipriani, Sofat.

Administrative, technical, or material support: Kuan, Tufail.

Supervision: Hingorani, Tufail, Sofat.

Conflict of Interest Disclosures: Dr Kuan reports grants from Dunhill Medical Trust. Dr Tufail reports personal fees from Apellis, Bayer, Genentech/Roche, IVERIC Bio, and Heidelberg Engineering, and personal fees and grants from Novartis. No other disclosures were reported.

Funding/Support: Dr Kuan is funded by the Dunhill Medical Trust (RPGF1806\67). Dr Warwick is supported by the Wellcome Trust (220558/Z/20/Z). Dr Hingorani is supported by a BHF Research Accelerator Award (AA/18/6/34223). Dr Tufail is supported by the National Institute for Health Research to Moorfields Eye Hospital and the Biomedical Research Centre for Ophthalmology. Dr Burgess is supported by Sir Henry Dale Fellowship, jointly funded by the Wellcome Trust and the Royal Society (204623/Z/16/Z) Dr Sofat is supported by the National Institute for Health Research, University College London Hospitals Biomedical Research Centre. This research was supported by the NIHR Cambridge Biomedical Research Centre (BRC-1215-20014).

Role of the Funder/Sponsor: The funders had no role in the design and conduct of the study; collection, management, analysis, and interpretation of the data; preparation, review, or approval of the manuscript; or decision to submit the manuscript for publication.

The International AMD Genomics Consortium (IAMDGC): The group members are listed in Supplement 2.

Disclaimer: The views expressed are those of the authors and not necessarily those of the National Institute for Health Research or the Department of Health and Social Care.

References
1.
Li  JQ, Welchowski  T, Schmid  M, Mauschitz  MM, Holz  FG, Finger  RP.  Prevalence and incidence of age-related macular degeneration in Europe: a systematic review and meta-analysis.   Br J Ophthalmol. 2020;104(8):1077-1084. doi:10.1136/bjophthalmol-2019-314422PubMedGoogle ScholarCrossref
2.
Pennington  KL, DeAngelis  MM.  Epidemiology of age-related macular degeneration (AMD): associations with cardiovascular disease phenotypes and lipid factors.   Eye Vis (Lond). 2016;3:34. doi:10.1186/s40662-016-0063-5PubMedGoogle ScholarCrossref
3.
Mitchell  P, Liew  G, Gopinath  B, Wong  TY.  Age-related macular degeneration.   Lancet. 2018;392(10153):1147-1159. doi:10.1016/S0140-6736(18)31550-2PubMedGoogle ScholarCrossref
4.
Wong  WL, Su  X, Li  X,  et al.  Global prevalence of age-related macular degeneration and disease burden projection for 2020 and 2040: a systematic review and meta-analysis.   Lancet Glob Health. 2014;2(2):e106-e116. doi:10.1016/S2214-109X(13)70145-1PubMedGoogle ScholarCrossref
5.
Resnikoff  S, Pascolini  D, Etya’ale  D,  et al.  Global data on visual impairment in the year 2002.   Bull World Health Organ. 2004;82(11):844-851.PubMedGoogle Scholar
6.
Ferris  FL  III, Wilkinson  CP, Bird  A,  et al; Beckman Initiative for Macular Research Classification Committee.  Clinical classification of age-related macular degeneration.   Ophthalmology. 2013;120(4):844-851. doi:10.1016/j.ophtha.2012.10.036PubMedGoogle ScholarCrossref
7.
Finger  RP, Daien  V, Eldem  BM,  et al.  Anti-vascular endothelial growth factor in neovascular age-related macular degeneration—a systematic review of the impact of anti-VEGF on patient outcomes and healthcare systems.   BMC Ophthalmol. 2020;20(1):294. doi:10.1186/s12886-020-01554-2PubMedGoogle ScholarCrossref
8.
Rofagha  S, Bhisitkul  RB, Boyer  DS, Sadda  SR, Zhang  K; SEVEN-UP Study Group.  Seven-year outcomes in ranibizumab-treated patients in ANCHOR, MARINA, and HORIZON: a multicenter cohort study (SEVEN-UP).   Ophthalmology. 2013;120(11):2292-2299. doi:10.1016/j.ophtha.2013.03.046PubMedGoogle ScholarCrossref
9.
Lanzetta  P, Loewenstein  A; Vision Academy Steering Committee.  Fundamental principles of an anti-VEGF treatment regimen: optimal application of intravitreal anti-vascular endothelial growth factor therapy of macular diseases.   Graefes Arch Clin Exp Ophthalmol. 2017;255(7):1259-1273. doi:10.1007/s00417-017-3647-4PubMedGoogle ScholarCrossref
10.
Smith  W, Assink  J, Klein  R,  et al.  Risk factors for age-related macular degeneration: pooled findings from three continents.   Ophthalmology. 2001;108(4):697-704. doi:10.1016/S0161-6420(00)00580-7PubMedGoogle ScholarCrossref
11.
Mitchell  P, Wang  JJ, Smith  W, Leeder  SR.  Smoking and the 5-year incidence of age-related maculopathy: the Blue Mountains Eye Study.   Arch Ophthalmol. 2002;120(10):1357-1363. doi:10.1001/archopht.120.10.1357PubMedGoogle ScholarCrossref
12.
Lambert  NG, ElShelmani  H, Singh  MK,  et al.  Risk factors and biomarkers of age-related macular degeneration.   Prog Retin Eye Res. 2016;54:64-102. doi:10.1016/j.preteyeres.2016.04.003PubMedGoogle ScholarCrossref
13.
Adams  MK, Chong  EW, Williamson  E,  et al.  20/20—Alcohol and age-related macular degeneration: the Melbourne Collaborative Cohort Study.   Am J Epidemiol. 2012;176(4):289-298. doi:10.1093/aje/kws004PubMedGoogle ScholarCrossref
14.
Boekhoorn  SS, Vingerling  JR, Hofman  A, de Jong  PT.  Alcohol consumption and risk of aging macula disorder in a general population: the Rotterdam Study.   Arch Ophthalmol. 2008;126(6):834-839. doi:10.1001/archopht.126.6.834PubMedGoogle ScholarCrossref
15.
Fraser-Bell  S, Wu  J, Klein  R, Azen  SP, Varma  R.  Smoking, alcohol intake, estrogen use, and age-related macular degeneration in Latinos: the Los Angeles Latino Eye Study.   Am J Ophthalmol. 2006;141(1):79-87. doi:10.1016/j.ajo.2005.08.024PubMedGoogle ScholarCrossref
16.
Knudtson  MD, Klein  R, Klein  BE.  Alcohol consumption and the 15-year cumulative incidence of age-related macular degeneration.   Am J Ophthalmol. 2007;143(6):1026-1029. doi:10.1016/j.ajo.2007.01.036PubMedGoogle ScholarCrossref
17.
Zhang  QY, Tie  LJ, Wu  SS,  et al.  Overweight, obesity, and risk of age-related macular degeneration.   Invest Ophthalmol Vis Sci. 2016;57(3):1276-1283. doi:10.1167/iovs.15-18637PubMedGoogle ScholarCrossref
18.
Howard  KP, Klein  BE, Lee  KE, Klein  R.  Measures of body shape and adiposity as related to incidence of age-related eye diseases: observations from the Beaver Dam Eye Study.   Invest Ophthalmol Vis Sci. 2014;55(4):2592-2598. doi:10.1167/iovs.15-18637Google ScholarCrossref
19.
Chakravarthy  U, Wong  TY, Fletcher  A,  et al.  Clinical risk factors for age-related macular degeneration: a systematic review and meta-analysis.   BMC Ophthalmol. 2010;10:31. doi:10.1186/1471-2415-10-31PubMedGoogle ScholarCrossref
20.
Katsi  VK, Marketou  ME, Vrachatis  DA,  et al.  Essential hypertension in the pathogenesis of age-related macular degeneration: a review of the current evidence.   J Hypertens. 2015;33(12):2382-2388. doi:10.1097/HJH.0000000000000766PubMedGoogle ScholarCrossref
21.
Ghaem Maralani  H, Tai  BC, Wong  TY,  et al.  Metabolic syndrome and risk of age-related macular degeneration.   Retina. 2015;35(3):459-466. doi:10.1097/IAE.0000000000000338PubMedGoogle ScholarCrossref
22.
Cougnard-Grégoire  A, Delyfer  MN, Korobelnik  JF,  et al.  Long-term blood pressure and age-related macular degeneration: the ALIENOR study.   Invest Ophthalmol Vis Sci. 2013;54(3):1905-1912. doi:10.1167/iovs.12-10192PubMedGoogle ScholarCrossref
23.
Chakravarthy  U, Bailey  CC, Scanlon  PH,  et al.  Progression from early/intermediate to advanced forms of age-related macular degeneration in a large UK cohort: rates and risk factors.   Ophthalmol Retina. 2020;4(7):662-672. doi:10.1016/j.oret.2020.01.012PubMedGoogle ScholarCrossref
24.
Bikbov  MM, Zainullin  RM, Gilmanshin  TR,  et al.  Prevalence and associated factors of age-related macular degeneration in a Russian population: the Ural Eye and Medical Study.   Am J Ophthalmol. 2020;210:146-157. doi:10.1016/j.ajo.2019.10.004PubMedGoogle ScholarCrossref
25.
Chen  X, Rong  SS, Xu  Q,  et al.  Diabetes mellitus and risk of age-related macular degeneration: a systematic review and meta-analysis.   PLoS One. 2014;9(9):e108196. doi:10.1371/journal.pone.0108196PubMedGoogle Scholar
26.
Heesterbeek  TJ, Lorés-Motta  L, Hoyng  CB, Lechanteur  YTE, den Hollander  AI.  Risk factors for progression of age-related macular degeneration.   Ophthalmic Physiol Opt. 2020;40(2):140-170. doi:10.1111/opo.12675PubMedGoogle ScholarCrossref
27.
Colijn  JM, den Hollander  AI, Demirkan  A,  et al; European Eye Epidemiology Consortium; EYE-RISK Consortium.  Increased high-density lipoprotein levels associated with age-related macular degeneration: evidence from the EYE-RISK and European Eye Epidemiology Consortia.   Ophthalmology. 2019;126(3):393-406. doi:10.1016/j.ophtha.2018.09.045PubMedGoogle ScholarCrossref
28.
Age-Related Eye Disease Study Research Group.  A randomized, placebo-controlled, clinical trial of high-dose supplementation with vitamins C and E, beta carotene, and zinc for age-related macular degeneration and vision loss: AREDS report no. 8.   Arch Ophthalmol. 2001;119(10):1417-1436. doi:10.1001/archopht.119.10.1417PubMedGoogle ScholarCrossref
29.
Age-Related Eye Disease Study 2 Research Group.  Lutein + zeaxanthin and omega-3 fatty acids for age-related macular degeneration: the Age-Related Eye Disease Study 2 (AREDS2) randomized clinical trial.   JAMA. 2013;309(19):2005-2015. doi:10.1001/jama.2013.4997PubMedGoogle ScholarCrossref
30.
Chew  EY, Clemons  TE, Sangiovanni  JP,  et al; Age-Related Eye Disease Study 2 (AREDS2) Research Group.  Secondary analyses of the effects of lutein/zeaxanthin on age-related macular degeneration progression: AREDS2 report no. 3.   JAMA Ophthalmol. 2014;132(2):142-149. doi:10.1001/jamaophthalmol.2013.7376PubMedGoogle Scholar
31.
Smith  GD, Timpson  N, Ebrahim  S.  Strengthening causal inference in cardiovascular epidemiology through mendelian randomization.   Ann Med. 2008;40(7):524-541. doi:10.1080/07853890802010709PubMedGoogle ScholarCrossref
32.
Hingorani  A, Humphries  S.  Nature’s randomised trials.   Lancet. 2005;366(9501):1906-1908. doi:10.1016/S0140-6736(05)67767-7PubMedGoogle ScholarCrossref
33.
Burgess  S, Davey Smith  G.  Mendelian randomization implicates high-density lipoprotein cholesterol-associated mechanisms in etiology of age-related macular degeneration.   Ophthalmology. 2017;124(8):1165-1174. doi:10.1016/j.ophtha.2017.03.042PubMedGoogle ScholarCrossref
34.
Fan  Q, Maranville  JC, Fritsche  L,  et al.  HDL-cholesterol levels and risk of age-related macular degeneration: a multiethnic genetic study using mendelian randomization.   Int J Epidemiol. 2017;46(6):1891-1902. doi:10.1093/ije/dyx189PubMedGoogle ScholarCrossref
35.
Fritsche  LG, Igl  W, Bailey  JN,  et al.  A large genome-wide association study of age-related macular degeneration highlights contributions of rare and common variants.   Nat Genet. 2016;48(2):134-143. doi:10.1038/ng.3448PubMedGoogle ScholarCrossref
36.
Bowden  J, Davey Smith  G, Haycock  PC, Burgess  S.  Consistent estimation in mendelian randomization with some invalid instruments using a weighted median estimator.   Genet Epidemiol. 2016;40(4):304-314. doi:10.1002/gepi.21965PubMedGoogle ScholarCrossref
37.
Bowden  J, Davey Smith  G, Burgess  S.  Mendelian randomization with invalid instruments: effect estimation and bias detection through Egger regression.   Int J Epidemiol. 2015;44(2):512-525. doi:10.1093/ije/dyv080PubMedGoogle ScholarCrossref
38.
Verbanck  M, Chen  CY, Neale  B, Do  R.  Detection of widespread horizontal pleiotropy in causal relationships inferred from mendelian randomization between complex traits and diseases.   Nat Genet. 2018;50(5):693-698. doi:10.1038/s41588-018-0099-7PubMedGoogle ScholarCrossref
39.
Wootton  RE, Richmond  RC, Stuijfzand  BG,  et al.  Evidence for causal effects of lifetime smoking on risk for depression and schizophrenia: a mendelian randomisation study.   Psychol Med. 2020;50(14):2435-2443. doi:10.1017/S0033291719002678PubMedGoogle ScholarCrossref
40.
Bowden  J, Holmes  MV.  Meta-analysis and mendelian randomization: a review.   Res Synth Methods. 2019;10(4):486-496. Published online April 23, 2019. doi:10.1002/jrsm.1346PubMedGoogle ScholarCrossref
41.
Seddon  JM, Silver  RE, Kwong  M, Rosner  B.  Risk prediction for progression of macular degeneration: 10 common and rare genetic variants, demographic, environmental, and macular covariates.   Invest Ophthalmol Vis Sci. 2015;56(4):2192-2202. doi:10.1167/iovs.14-15841PubMedGoogle ScholarCrossref
42.
Wang  JJ, Rochtchina  E, Smith  W,  et al.  Combined effects of complement factor H genotypes, fish consumption, and inflammatory markers on long-term risk for age-related macular degeneration in a cohort.   Am J Epidemiol. 2009;169(5):633-641. doi:10.1093/aje/kwn358PubMedGoogle ScholarCrossref
43.
Jonasson  F, Fisher  DE, Eiriksdottir  G,  et al.  Five-year incidence, progression, and risk factors for age-related macular degeneration: the age, gene/environment susceptibility study.   Ophthalmology. 2014;121(9):1766-1772. doi:10.1016/j.ophtha.2014.03.013PubMedGoogle ScholarCrossref
44.
Vingerling  JR, Hofman  A, Grobbee  DE, de Jong  PT.  Age-related macular degeneration and smoking. the Rotterdam Study.   Arch Ophthalmol. 1996;114(10):1193-1196. doi:10.1001/archopht.1996.01100140393005PubMedGoogle ScholarCrossref
45.
Khandhadia  S, Lotery  A.  Oxidation and age-related macular degeneration: insights from molecular biology.   Expert Rev Mol Med. 2010;12:e34. doi:10.1017/S146239941000164XPubMedGoogle Scholar
46.
Alberg  A.  The influence of cigarette smoking on circulating concentrations of antioxidant micronutrients.   Toxicology. 2002;180(2):121-137. doi:10.1016/S0300-483X(02)00386-4PubMedGoogle ScholarCrossref
47.
Chang  MA, Bressler  SB, Munoz  B, West  SK.  Racial differences and other risk factors for incidence and progression of age-related macular degeneration: Salisbury Eye Evaluation (SEE) project.   Invest Ophthalmol Vis Sci. 2008;49(6):2395-2402. doi:10.1167/iovs.07-1584PubMedGoogle ScholarCrossref
48.
Khan  JC, Thurlby  DA, Shahid  H,  et al; Genetic Factors in AMD Study.  Smoking and age related macular degeneration: the number of pack years of cigarette smoking is a major determinant of risk for both geographic atrophy and choroidal neovascularisation.   Br J Ophthalmol. 2006;90(1):75-80. doi:10.1136/bjo.2005.073643PubMedGoogle ScholarCrossref
49.
Thornton  J, Edwards  R, Mitchell  P, Harrison  RA, Buchan  I, Kelly  SP.  Smoking and age-related macular degeneration: a review of association.   Eye (Lond). 2005;19(9):935-944. doi:10.1038/sj.eye.6701978PubMedGoogle ScholarCrossref
50.
Ciulla  TA, Harris  A, Martin  BJ.  Ocular perfusion and age-related macular degeneration.   Acta Ophthalmol Scand. 2001;79(2):108-115. doi:10.1034/j.1600-0420.2001.079002108.xPubMedGoogle ScholarCrossref
51.
Suñer  IJ, Espinosa-Heidmann  DG, Marin-Castano  ME, Hernandez  EP, Pereira-Simon  S, Cousins  SW.  Nicotine increases size and severity of experimental choroidal neovascularization.   Invest Ophthalmol Vis Sci. 2004;45(1):311-317. doi:10.1167/iovs.03-0733PubMedGoogle ScholarCrossref
52.
Akishima  S, Matsushita  S, Sato  F,  et al.  Cigarette-smoke-induced vasoconstriction of peripheral arteries: evaluation by synchrotron radiation microangiography.   Circ J. 2007;71(3):418-422. doi:10.1253/circj.71.418PubMedGoogle ScholarCrossref
53.
Aiello  LP, Northrup  JM, Keyt  BA, Takagi  H, Iwamoto  MA.  Hypoxic regulation of vascular endothelial growth factor in retinal cells.   Arch Ophthalmol. 1995;113(12):1538-1544. doi:10.1001/archopht.1995.01100120068012PubMedGoogle ScholarCrossref
54.
Kunchithapautham  K, Atkinson  C, Rohrer  B.  Smoke exposure causes endoplasmic reticulum stress and lipid accumulation in retinal pigment epithelium through oxidative stress and complement activation.   J Biol Chem. 2014;289(21):14534-14546. doi:10.1074/jbc.M114.564674PubMedGoogle ScholarCrossref
55.
Wang  L, Kondo  N, Cano  M,  et al.  Nrf2 signaling modulates cigarette smoke-induced complement activation in retinal pigmented epithelial cells.   Free Radic Biol Med. 2014;70:155-166. doi:10.1016/j.freeradbiomed.2014.01.015PubMedGoogle ScholarCrossref
56.
Gibson  J, Hakobyan  S, Cree  AJ,  et al.  Variation in complement component C1 inhibitor in age-related macular degeneration.   Immunobiology. 2012;217(2):251-255. doi:10.1016/j.imbio.2011.07.015PubMedGoogle ScholarCrossref
57.
Bird  AC.  Therapeutic targets in age-related macular disease.   J Clin Invest. 2010;120(9):3033-3041. doi:10.1172/JCI42437PubMedGoogle ScholarCrossref
58.
Ambati  J, Atkinson  JP, Gelfand  BD.  Immunology of age-related macular degeneration.   Nat Rev Immunol. 2013;13(6):438-451. doi:10.1038/nri3459PubMedGoogle ScholarCrossref
59.
Chong  EW, Kreis  AJ, Wong  TY, Simpson  JA, Guymer  RH.  Alcohol consumption and the risk of age-related macular degeneration: a systematic review and meta-analysis.   Am J Ophthalmol. 2008;145(4):707-715. doi:10.1016/j.ajo.2007.12.005PubMedGoogle ScholarCrossref
60.
Dinu  M, Pagliai  G, Casini  A, Sofi  F.  Food groups and risk of age-related macular degeneration: a systematic review with meta-analysis.   Eur J Nutr. 2019;58(5):2123-2143. doi:10.1007/s00394-018-1771-5PubMedGoogle ScholarCrossref
61.
Obisesan  TO, Hirsch  R, Kosoko  O, Carlson  L, Parrott  M.  Moderate wine consumption is associated with decreased odds of developing age-related macular degeneration in NHANES-1.   J Am Geriatr Soc. 1998;46(1):1-7. doi:10.1111/j.1532-5415.1998.tb01005.xPubMedGoogle ScholarCrossref
62.
Das  SK, Vasudevan  DM.  Alcohol-induced oxidative stress.   Life Sci. 2007;81(3):177-187. doi:10.1016/j.lfs.2007.05.005PubMedGoogle ScholarCrossref
63.
Cederbaum  AI.  Role of lipid peroxidation and oxidative stress in alcohol toxicity .  Free Radic Biol Med. 1989;7(5):537-539. doi:10.1016/0891-5849(89)90029-4PubMedGoogle ScholarCrossref
64.
Klein  R, Myers  CE, Klein  BE.  Vasodilators, blood pressure-lowering medications, and age-related macular degeneration: the Beaver Dam Eye Study.   Ophthalmology. 2014;121(8):1604-1611. doi:10.1016/j.ophtha.2014.03.005PubMedGoogle ScholarCrossref
65.
Cummings  M, Cunha-Vaz  J.  Treatment of neovascular age-related macular degeneration in patients with diabetes.   Clin Ophthalmol. 2008;2(2):369-375. doi:10.2147/OPTH.S2560PubMedGoogle Scholar
66.
Sander  B, Larsen  M, Moldow  B, Lund-Andersen  H.  Diabetic macular edema: passive and active transport of fluorescein through the blood-retina barrier.   Invest Ophthalmol Vis Sci. 2001;42(2):433-438.PubMedGoogle Scholar
67.
Burgess  S, Scott  RA, Timpson  NJ, Davey Smith  G, Thompson  SG; EPIC- InterAct Consortium.  Using published data in mendelian randomization: a blueprint for efficient identification of causal risk factors.   Eur J Epidemiol. 2015;30(7):543-552. doi:10.1007/s10654-015-0011-zPubMedGoogle ScholarCrossref
68.
Lawlor  DA.  Commentary: two-sample mendelian randomization: opportunities and challenges.   Int J Epidemiol. 2016;45(3):908-915. doi:10.1093/ije/dyw127PubMedGoogle ScholarCrossref
69.
Burgess  S, Davey Smith  G, Davies  NM,  et al.  Guidelines for performing mendelian randomization investigations.   Wellcome Open Res. 2020;4:186. doi:10.12688/wellcomeopenres.15555.2PubMedGoogle ScholarCrossref
70.
Didelez  V, Sheehan  N.  Mendelian randomization as an instrumental variable approach to causal inference.   Stat Methods Med Res. 2007;16(4):309-330. doi:10.1177/0962280206077743PubMedGoogle ScholarCrossref
71.
VanderWeele  TJ, Tchetgen Tchetgen  EJ, Cornelis  M, Kraft  P.  Methodological challenges in mendelian randomization.   Epidemiology. 2014;25(3):427-435. doi:10.1097/EDE.0000000000000081PubMedGoogle ScholarCrossref
72.
Davies  NM, Holmes  MV, Davey Smith  G.  Reading mendelian randomisation studies: a guide, glossary, and checklist for clinicians.   BMJ. 2018;362:k601. doi:10.1136/bmj.k601PubMedGoogle Scholar
73.
Burgess  S, Bowden  J, Fall  T, Ingelsson  E, Thompson  SG.  Sensitivity analyses for robust causal inference from mendelian randomization analyses with multiple genetic variants.   Epidemiology. 2017;28(1):30-42. doi:10.1097/EDE.0000000000000559PubMedGoogle ScholarCrossref
74.
Slob  EAW, Burgess  S.  A comparison of robust mendelian randomization methods using summary data.   Genet Epidemiol. 2020;44(4):313-329. doi:10.1002/gepi.22295PubMedGoogle ScholarCrossref
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