R. NICKBRYANMDS. JAMESZINREICHMD
The computed tomographic scan revealed a dense bony lesion involving the right ethmoidal sinus. The frontal sinus was not involved, and extension of the lesion did not include the cribriform plate, lamina papyracea, or orbit. The specimen was removed during limited functional endoscopic sinus surgery and inferior turbinate reduction.
The inherited adenomatous polyposis syndromes, including Gardner syndrome and familial polyposis coli, have a known association with osteomas and other soft tissue tumors, such as dermoid cysts and fibromas.1 Familial polyposis coli and Gardner syndrome most likely represent the same disease process. There is a dominant mode of inheritance, and facial signs and symptoms are often the initial presentation. Extracolonic manifestations, which include polyps of the stomach and small bowel, fibrous tumors, skin and skeletal abnormalities, and dental abnormalities, may precede the diagnosis of colonic polyps. Because of the significant chance of malignant degeneration of the colonic polyps, appropriate diagnosis remains crucial. If colonic polyps are not treated, colorectal carcinoma will usually develop.
Imaging Quiz Case 1. Arch Otolaryngol Head Neck Surg. 1998;124(5):604. doi:10.1001/archotol.124.5.602
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