Systemic autoinflammatory disorders commonly present in the head and neck. Bullous pemphigoid (BP) is an autoinflammatory blistering disorder characterized by deposition of antihemidesmosomal antibodies at the dermal-epidermal junction.1 Classically, patients present with pruritic, tense bullae in a symmetric pattern over the trunk and intertriginous areas. Up to 30% of patients have mucosal involvement, most commonly of the gingiva or buccal mucosa.2
Faraji F, Crawford K, Stramiello CJ, Jafari A, Weissbrod PA, Brumund KT. Bullous Pemphigoid Presenting as Oropharyngeal Hemorrhage. JAMA Otolaryngol Head Neck Surg. 2019;145(3):288–290. doi:10.1001/jamaoto.2018.4051
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