Kaposiform Hemangioendothelioma of Internal Auditory Canal Presenting in 4-Week-Old Newborn

Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor. It is classified by the World Health Organization (WHO) as intermediate malignant.¹ Some cases have been associated with Kasabach-Merritt syndrome (KMS), a phenomenon defined by thrombocytopenia and coagulopathy, increasing the risk for life-threatening hemorrhage.^1,2 Typically, KHE is found in pediatric patients.¹ The most common locations for presentation are the extremities, trunk, and retroperitoneum. A smaller number of cases have been reported in the head and neck.³ To our knowledge, there has been only 1 previous report of KHE in the internal auditory canal.⁴ We present what we believe to be the youngest patient with an internal auditory canal KHE.