Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor. It is classified by the World Health Organization (WHO) as intermediate malignant.1 Some cases have been associated with Kasabach-Merritt syndrome (KMS), a phenomenon defined by thrombocytopenia and coagulopathy, increasing the risk for life-threatening hemorrhage.1,2 Typically, KHE is found in pediatric patients.1 The most common locations for presentation are the extremities, trunk, and retroperitoneum. A smaller number of cases have been reported in the head and neck.3 To our knowledge, there has been only 1 previous report of KHE in the internal auditory canal.4 We present what we believe to be the youngest patient with an internal auditory canal KHE.
Colasacco CJ, Stidham K, Graifman G, et al. Kaposiform Hemangioendothelioma of Internal Auditory Canal Presenting in 4-Week-Old Newborn. JAMA Otolaryngol Head Neck Surg. 2022;148(3):282–284. doi:10.1001/jamaoto.2021.4010
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