Meningiomas are a heterogeneous group of central nervous system tumors arising from the arachnoidal cap cells of the meninges, and they represent approximately 15% to 20% of all primary intracranial neoplasms.1The WHO currently recognizes 13 histologic subtypes.2Clear cell meningioma is an uncommon variant, representing approximately 0.2% of all meningiomas.3It is most commonly found in the spinal or cerebellopontine region and usually affects younger patients. This histologic subtype shows aggressive behavior, with a high recurrence rate, and distant metastasis, though rare, has been reported.4