Polyotia is an extremely rare congenital anomaly of the external ear. While 5 cases have been documented in the literature, only one case of isolated polyotia has been reported to date. We present a case of isolated polyotia in which a child's right auricle was duplicated as a mirror image. The duplicated portion of the affected ear was positioned anteriorly and was approximately the same size as the normal ear. There were 2 fully developed helices, antihelices, and conchae. There was one partially developed tragus and a single narrow external auditory meatus. There were no other congenital anomalies and the child was developmentally normal.