[Skip to Content]
Access to paid content on this site is currently suspended due to excessive activity being detected from your IP address Please contact the publisher to request reinstatement.
[Skip to Content Landing]
Citations 0
Clinical Problem Solving: Radiology
January 18, 2010

Radiology Quiz Case 1

Author Affiliations

Copyright 2010 American Medical Association. All Rights Reserved. Applicable FARS/DFARS Restrictions Apply to Government Use.2010

Arch Otolaryngol Head Neck Surg. 2010;136(1):95. doi:10.1001/archoto.2009.182-a

A 7-year-old boy with a history of Hunter syndrome presented to the emergency department with a 3-day history of difficulty breathing. His parents noted that he had been in his usual state of health until 3 days before presentation, when he developed a slight cough, which worsened and was described as “barking” in nature approximately 24 hours before admission.

Physical examination revealed an afebrile, intermittently sedated child who became agitated and combative when aroused. His oral cavity was notable for macroglossia and copious secretions. His oropharynx was normal in appearance, and there was mucopurulent drainage from his nose. He had a short neck, growth delay, and an abnormal facies. He was initially treated with multiple courses of albuterol sulfate, which he used at home for his asthma. He did not improve with this treatment, and a chest x-ray film was obtained (Figure 1and Figure 2). He was admitted to the pediatric intensive care unit and treated aggressively with continuous positive airway pressure and intravenous steroids.