R. NICKBRYANMDS. JAMESZINREICHMD
A 17-MONTH-OLD boy was noted by his parents to have poor hearing since birth. The child did not have any of the stigmata of the high-risk registry for hearing loss except that his older brother also had bilateral sensorineural hearing loss. His parents were unsure whether he had any vestibular disturbances. Sound field testing demonstrated a downward-sloping moderate to severe hearing loss, which was confirmed by auditory brain evoked response testing, which revealed a bilateral flat moderate hearing loss. A computed tomographic scan of the temporal bone was obtained (Figure 1 and Figure 2).
Dennis Lee, Stanley Stutz, James Coticchia, Charles D. Bluestone. Quiz Case 2. Arch Otolaryngol Head Neck Surg. 1999;125(7):813. doi: