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Radiology Forum
September 1999

Quiz Case 2

Author Affiliations


Arch Otolaryngol Head Neck Surg. 1999;125(9):1037-1039. doi:

Progressive hemifacial atrophy is a rare disorder characterized by a slow, progressive facial atrophy of subcutaneous fat that can be followed by the wasting of associated skin, cartilage, connective tissue, muscle, and bone.1 It includes an active progressive phase (2-10 years), followed by a burning out of the atrophic process, with subsequent stability. Some authors report a predilection for the left side of the face.2 Bilateral manifestations have been reported in 5% to 10% of the cases, and ipsilateral body involvement is rarely found.3 The disorder has a female-male ratio of 3:2. The initial site of atrophy is variable, with the modiolus area being the most common.

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