The finding of nasal polyps is common and ordinarily does not provoke unusual interest in the rhinologist. He expects to encounter them frequently in allergic and vasomotor nasal disturbances and in some types of suppurative sinal disease, especially ethmoiditis. Less often he finds them in association with malignant growths of the nose and sinuses, nasopharyngeal fibromas, syphilis, lupus and foreign bodies. He recognizes the etiologic relation of a solitary choanal polyp to diseased antral mucous membrane.
Experience, moreover, has taught him that nasal polyposis is almost exclusively a disease of adult life, except the choanal form, which not infrequently occurs in children. The finding of extensive multiple polyps in childhood would in itself be unusual, but its association with extreme external nasal deformity should stamp the case as worthy of study. This impression gains strength in view of the surprisingly few references to the syndrome in the literature.
Covili-Faggioli1 credited