Lipoid granulomatosis (type Hand-Schüller-Christian disease) occurring in an adult and with diffuse involvement of the middle ear and temporal bone as the sole manifestation of the disease is uncommon. The relative rarity of the condition as evidenced by the paucity of reports in the literature, as well as the extreme difficulty of establishing the diagnosis in this case and the excellent therapeutic result after intensive roentgen therapy, warrant the present report as well as a brief discussion of lipoid granulomatosis.
REPORT OF A CASE
R. H., a woman aged 50, was first observed in the outpatient clinic of the Mount Sinai Hospital on Jan. 6, 1936, with the chief complaint of gradual onset of pain and deafness in the left ear of four years' duration. The pain, which had become continuous, was accompanied by buzzing. Four months prior to admission the patient suffered episodes of transitory facial paralysis and postauricular
ROSENWASSER H. LIPOID GRANULOMATOSIS (HAND-SCHÜLLER-CHRISTIAN DISEASE) INVOLVING THE MIDDLE EAR AND TEMPORAL BONE. Arch Otolaryngol. 1940;32(6):1045–1053. doi:10.1001/archotol.1940.00660021053005
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