The unusual combination of a common pyogenic infection and a rare and infrequent metabolic disturbance of the bones of the skull has prompted the following report of a case of Schüller-Christian disease.
The basis on which acute streptococcic otitis media and mastoiditis developed in a child 3 years old was felt to be impaired nutrition of the temporal bone. The case presented the usual problem of a simple mastoidectomy. After the evacuation of the postaural abscess, the mastoid cortex was found to be a sequestrum, which was easily removed, with most of the mastoid cells. This was thought to be unusual, and after the completion of the operation, roentgenograms of the skull were taken, which revealed the presence of Schüller-Christian disease involving both sides of the skull, as shown in figure 1. The opposite ear had not shown any evidence of an acute infection, even though roentgenograms revealed a similar
COOPER KG. ACUTE MASTOIDITIS COMPLICATED BY SCHÜLLER-CHRISTIAN DISEASE. Arch Otolaryngol. 1941;33(6):1028–1032. doi:10.1001/archotol.1941.00660031039011