The osseous structures of the head are capable of undergoing pathologic changes which are of interest to the otolaryngologist. The bony labyrinth of the ear, for example, may be affected by such diseases as fragilitas ossium, osteitis deformans, osteoarthritis, osteogenesis imperfecta, osteomalacia, osteopsathyrosis, rickets, Paget's disease, senile osteoporosis, chondrodystrophy and athyreopituitary dwarfism. Many of these may affect any and all parts of the skull. There is a group of idiopathic hyperostoses of the skull, which have long been considered rare, viz., osteitis deformans, or Paget's disease, and craniosclerosis, or leontiasis ossea. Recently Coppo,1 in connection with a description of a patient with the latter condition, reviewed the literature extensively and found the cases recorded not numerous.
Virchow2 proposed the term "leontiasis ossea" for a particular form of hyperostosis of the skull. The name was suggested by the appearance which the face of the patient came to assume, due to enlargement
LEDERER FL. IDIOPATHIC HYPEROSTOSIS OF THE SKULL. Arch Otolaryngol. 1941;34(1):88–98. doi:10.1001/archotol.1941.00660040098009
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