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January 1959

Congenital Micrognathia

Author Affiliations

Berkeley, Calif.
From the Department of Otolaryngology, Children's Hospital of the East Bay, Oakland, Calif.

AMA Arch Otolaryngol. 1959;69(1):31-44. doi:10.1001/archotol.1959.00730030035005

Introduction  Pierre Robin,25 in 1923, published a paper describing a syndrome encountered in the newborn, consisting of hypoplasia of the mandible, glossoptosis, and consequent respiratory and feeding difficulty. The anatomy pertinent to this syndrome is seen in Figure 1, which illustrates the attachment of the genioglossus muscle to the symphysis of the mandible. Shortening of the mandibular arch permits the tongue to fall back and thereby reduce the size of the hypopharynx. This condition is known as the Pierre Robin syndrome, and is referred to variously as "micrognathia," "micrognathy," "hypoplasia of the mandible," "receding chin and glossoptosis," "micrognathia with obstruction," and "ateliosis of the mandible."Respiratory obstruction is the most important feature of this syndrome. If the obstruction is not satisfactorily relieved by placing the patient on his side or face, or if feeding is accompanied by repeated episodes of aspiration, the patient is in grave danger. It is