There are many congenital vascular deformities of the superior mediastinum. They are of increasing importance, in so far as, when recognized, they can now be brought under surgical attack. In many instances, the obstructive symptoms of the vital passages of the trachea and esophagus can be successfully relieved. There are many of these deformities, however, which are nearly impossible to diagnose or relieve.
Agenesis of the lung with tracheal stenosis is another congenital defect rarely seen. Putney and Baltzell1 stated that diagnosis during life is infrequent. Most cases are stillborn with this defect or die during infancy with respiratory disease. Wexels2 collected reports on 87 cases. Thirty-eight had been diagnosed during life. Thirteen were verified at autopsy. Fifteen were still alive as of the time of his report. It is reported that one-half of these cases have other congenital defects, e.g., atresia of larynx, imperforate anus, and patent
FAHEY DJ. Unusual Congenital Deformity of the Superior Mediastinum. AMA Arch Otolaryngol. 1960;72(1):102–103. doi:10.1001/archotol.1960.00740010106018
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