DEAFNESS has been recognized as a major symptom in Paget's disease of the skull for over half a century. In Fowler's1 series of 99 cases deafness was the initial symptom in three patients, but it was a major symptom in 41 at a later stage of the disease. In this series tinnitus was present in ten patients and vertigo in 23 patients. Hearing loss associated with Paget's disease has been usually identified as "nerve deafness." Lindsay and Perlman,2 however, reported two cases with marked conductive deafness out of four patients with definite impairment of hearing.
Although conductive deafness has been a frequent target for microsurgery in recent years, Paget's disease has not been in the focus of attention of research. During the last ten years only one paper was published (Griffey3), with description of histological changes in the labyrinth of one patient.
Diagnosis is made by
WALTNER JG. Stapedectomy in Paget's Disease: Histological and Clinical Studies. Arch Otolaryngol. 1965;82(4):355–358. doi:10.1001/archotol.1965.00760010357004
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