ABSENCE of the oval window is apparently a very rare phenomenon. In spite of the large number of middle ear explorations that have been carried out since the introduction of stapes surgery a decade ago—as well as other types of middle ear procedures performed nowadays—only eight cases have thus far been reported.1-5 Presented below is a case of congenital absence of the oval window with additional congenital abnormalities of the ossicular chain and of the auricle.
Report of a Case
A 59-year-old white farmer was first presented at the Department of Otolaryngology and Maxillofacial Surgery, University of Iowa, on May 22, 1963, with a history of hearing loss in the right ear since childhood. During the past 10 to 15 years the hearing in both ears had gradually deteriorated, more so on the right side. Apart from a roaring tinnitus, he had no other concomitant symptoms. There was no
BERNSTEIN L. Congenital Absence of the Oval Window. Arch Otolaryngol. 1966;83(6):533–537. doi:10.1001/archotol.1966.00760020535007