THE AVAILABLE literature indicates there are two congenital anomalies which have been reported so infrequently as to be termed rare. These are salivary gland choristoma of the middle ear, a mass of tissue histologically normal for an organ or part of the body other than the site at which it is found, and congenital absence of the oval window. We are unable to find a reported case of the two conditions combined, although Noguera and Haase1 reported one case of a middle ear salivary gland choristoma associated with a deformed stapes and absent incus.
Taylor and Martin,2 as well as Steffen and House,3 reported a case of salivary gland choristoma of the middle ear diagnosed by exploratory tympanotomy and biopsy. They were unable to remove the tumor in its entirety because of undue risk to the facial nerve. In neither of these cases was a stapes visualized,
Caplinger CB, Hora JF. Middle Ear Choristoma With Absent Oval Window: A Report of One Case. Arch Otolaryngol. 1967;85(4):365–366. doi:10.1001/archotol.1967.00760040367004
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