THE EXISTENCE of congenital cholesteatomas is an accepted fact; only their frequency is undetermined. It is agreed that they are derived from a congenital epidermal cell rest, but according to Fernandez et al1 they are unimportant for practical purposes. Considering the facial nerve complications involved in the reported cases, which I believe to be of primary or congenital cholesteatomas, this statement is far from acceptable.
Report of Cases
Case 1.—A 9-year-old boy was first seen Dec 19, 1962. Eight weeks previously he had developed a paralysis on the right side of his face, associated with a one-day history of otalgia. He had a complete facial paralysis on the right side, his right tympanic membrane was rather lustrous in appearance, and he had a 15-db conductive hearing loss. There was no perforation of the pars flaccida or pars tensa, the latter being confirmed in my office by microscopic examination. Because of
Brosnan ML. Primary Cholesteatomas of the Temporal Bone. Arch Otolaryngol. 1967;86(4):363–366. doi:10.1001/archotol.1967.00760050365002
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