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February 1970

Madelung's Deformity With Conductive Hearing Loss

Author Affiliations

Beirut, Lebanon
From the Department of Otolaryngology, American University Hospital, Beirut, Lebanon.

Arch Otolaryngol. 1970;91(2):175-178. doi:10.1001/archotol.1970.00770040245014

THE dyschondrosteosis of Leri-Weill and the condition known as Madelung's deformity seem to be related entities.1 Dyschondrosteosis was first described in 1929 in the French literature by Leri and Weill.2 However, Madelung, a German surgeon, has described the deformity in a patient presented to the seventh congress of surgeons in Germany in 1878.3 A review of the available literature shows few reports of this deformity in recent years. Those in the European medical journals are more readily available. Stetten, in 1909, was the first to report the condition in the American literature with a complete review of its history.4

The condition of Leri-Weill is characterized by short stature of variable degree. The forearms and lower extremities are characteristically short (Fig 1). There is a posterior subluxation of the ulna and elbow with limited wrist motion, with or without genuvarus. X-ray film findings are those of an

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