Temporal bone findings in a 57-year-old man with hemochromatosis and chondrocalcinosis who died 5½ weeks poststapedectomy demonstrated virtually identical otosclerotic lesions in both ears. The operated side appeared functionally adequate. Focal degeneration of the otolithic membrane and macula of the saccule was present on both sides, but to an even greater degree on the unoperated side. Early focal degenerative changes were also present in the utricle macula and ampullae.
Otosclerosis of the stapediovestibular joint in a patient with hemochromatosis is of interest because of the presence of arthropathy (chondrocalcinosis). The possible predisposing role of calcific degenerative change of the oval window, with resultant otosclerotic repair, is mentioned.
Gussen R. Otosclerosis and Vestibular Degeneration. Arch Otolaryngol. 1973;97(6):484–487. doi:10.1001/archotol.1973.00780010498013
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