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Article
August 1973

Neurofibroma of the Larynx Occurring With Von Recklinghausen Disease: Report of a Case

Author Affiliations

Los Angeles
From the Department of Surgery/Head and Neck, UCLA School of Medicine, Los Angeles. Dr. Jafek is currently with the Department of Otolaryngology, Public Health Service Hospital, Baltimore.

Arch Otolaryngol. 1973;98(2):77-79. doi:10.1001/archotol.1973.00780020083002
Abstract

A case of neurofibroma of the larynx occurring with generalized neurofibromatosis (Von Recklinghausen disease) is reported and the literature reviewed. Typical signs include those of the generalized disease (cutaneous and visceral neurofibromas, café-au-lait spots, bony abnormalities, and mental deficiency) together with the symptoms of a slowly growing laryngeal mass, eg, dyspnea, hoarseness, and dysphagia.

The diagnosis is confirmed by direct laryngoscopy and biopsy. Small, encapsulated tumors may be completely excised at laryngoscopy, whereas larger, less well-encapsulated ones may require lateral thyrotomy or laryngofissure for complete removal.

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