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Clinical Notes
April 1976

Pachyonychia Congenita With Involvement of the Larynx

Author Affiliations

From the departments of otorhinolaryngology and communicative sciences (Drs Cohn and McFarlane), and dermatology (Dr Knox), Baylor College of Medicine, Houston.

Arch Otolaryngol. 1976;102(4):233-235. doi:10.1001/archotol.1976.00780090075011

• Pachyonychia congenita is a genetic syndrome of epithelial dysplasia that is inherited as an autosomal dominant trait. Its unique involvement within the larynx of a 3-year-old boy prompted this brief report of its clinical behavior and management.