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December 1976

Cochlear Nerve Degeneration Coincident With Adrenocerebroleukodystrophy

Author Affiliations

From the Department of Otorhinolaryngology and Communicative Sciences, Baylor College of Medicine, Houston.

Arch Otolaryngol. 1976;102(12):722-726. doi:10.1001/archotol.1976.00780170040003

• A 19-month-old boy had adrenocerebroleukodystrophy and unusually severe cochlear nerve degeneration and demyelination, a condition in advance of that expected from known disease entities. We report the only known temporal bone study in adrenocerebroleukodystrophy.

(Arch Otolaryngol 102:722-726, 1976)