• The hearing status of 18 patients with Morquio's syndrome (mucopolysaccharidosis IV) was evaluated. All three patients under age 8 years had a conductive hearing loss. Fourteen of 15 patients 8 years of age and older had a mixed or sensorineural hearing loss; one had normal hearing. Six patients wore hearing aids. By the end of the first decade of life, most persons with Morquio's syndrome may be expected to have either a mixed or sensorineural hearing loss. Amplification may be required.
(Arch Otolaryngol 103:518-520, 1977)
Erwin D. Riedner, L. Stefan Levin. Hearing Patterns in Morquio's Syndrome (Mucopolysaccharidosis IV). Arch Otolaryngol. 1977;103(9):518–520. doi:10.1001/archotol.1977.00780260048003