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August 1982

Anomalies of the Auditory Organ in Potter's SyndromeHistopathological Findings in the Temporal Bone

Arch Otolaryngol. 1982;108(8):484-488. doi:10.1001/archotol.1982.00790560022006

• Histopathological findings in the temporal bone are described in a newborn infant, diagnosed as having Potter's syndrome. The infant had severely malformed low-set ears bilaterally and a small lower jaw; autopsy findings showed bilateral renal agenesis and pulmonary hypoplasia. The temporal bone indicated the deformities of the inner ear, classified as Mondini-type, complicated by extensive deformities of the external ear and middle ear, including absence of auditory ossicles, atresia of the oval window, abnormal course of the facial nerve, and hypoplastic external auditory canal. The cochlear membranous labyrinth showed nearly normal form in the upper turn, but severe hypoplasia in the basal turn, which was an unusual cochlear anomaly.

(Arch Otolaryngol 1982;108:484-488)