• Inherited cochleosaccular dysplasia occurred in a woman coincidentally with Down's syndrome. Study of the right temporal bone revealed abnormalities of the cochlea and saccule consistent with Scheibe's original description. There was also a short cochlea and small lateral semicircular canal consistent with previous descriptions of Down's syndrome.
(Arch Otolaryngol 1984;110:477-479)
Walby AP, Schuknecht HF. Concomitant Occurrence of Cochleosaccular Dysplasia and Down's Syndrome. Arch Otolaryngol. 1984;110(7):477–479. doi:10.1001/archotol.1984.00800330059013
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