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March 1987

The Temporal Bone Anomaly in CHARGE Association

Author Affiliations

From the Department of Otolaryngology and Communication Sciences, State University of New York, Syracuse.

Arch Otolaryngol Head Neck Surg. 1987;113(3):321-324. doi:10.1001/archotol.1987.01860030097017

• Examination of the temporal bones from a patient with the CHARGE association revealed an unusual form of dysplasia. Mondini dysplasia of the pars inferior with complete absence of the pars superior was observed in both temporal bones. A review of the literature revealed four previous descriptions of this unique anomaly in patients whose clinical picture resembled the required components of CHARGE. On this basis, it is suggested that this anomaly represents a specific form of labyrinthine dysplasia which may be called the CHARGE dysplasia of the temporal bone.

(Arch Otolaryngol Head Neck Surg 1987;113:321-324)

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