To the Editor.—Twelve years ago, we described seven patients with a particular congenital deformity of the labyrinth of the inner ear, two of whom developed a cerebrospinal fluid fistula through the oval window.1 We agreed with Jensen who, in a previous article in the US literature,2 stated that this was not the defect described in detail by Carlo Mondini in 17913 but, rather, a more severe dysplasia. We have now seen 30 patients with this more severe type of dysplasia, 12 of whom have developed a spontaneous cerebrospinal fluid fistula through the inner ear or presented with meningitis. These cases have been described in various publications.4-7 Other European publications have described the difference between the true Mondini and the "pseudo-Mondini" deformity,8,9 although we consider the latter a term to be deprecated.10,11
We are dismayed, therefore, that so much confusion persists in the US
PHELPS PD, LLOYD GAS. Mondini Dysplasia Is Not Associated With Meningitis and Cerebrospinal Fluid Fistula. Arch Otolaryngol Head Neck Surg. 1991;117(8):931. doi:10.1001/archotol.1991.01870200125023
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