The points raised by Drs Phelps and Lloyd, acknowledged experts in temporal bone radiology, are appreciated. We would agree that distinguishing among the various types of morphogenetic deformities that can affect the inner ear is of the utmost importance. The problem becomes one of semantics. The traditional schemata used to classify congenital anomalies of the inner ear are based on only a few case reports; Michel1 reported a case in 1863; Mondini2 reported an example of an inner ear anomaly in 1791; Schiebe3,4 reported two cases in 1892 and 1895; and Alexander5 described a type of malformation in 1927.
Some of the limitations of this classification scheme have been explored in an excellent article by Jackler et al.6 Concentrating on the vast spectrum of morphogenetic defects, these investigators used polytomography and thinslice, high-resolution computed tomography to study development of the bony labyrinth. A more representative classification scheme for morphogenetic deformities
SMITH RJH, OHLMS LA, ALFORD BR, EDWARDS MS. Mondini Dysplasia Is Not Associated With Meningitis and Cerebrospinal Fluid Fistula-Reply. Arch Otolaryngol Head Neck Surg. 1991;117(8):931–932. doi:10.1001/archotol.1991.01870200125024
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