Recent reviews1 have emphasized the relatively frequent occurrence of sarcoma as a childhood disease and its importance in mortality figures. Congenital sarcoma, however, particularly sarcoma of the extremities, is rare. Steffen2 extensively reviewed the literature in 1905 and reported 219 cases of malignant tumors in infancy. He listed 19 cases of sarcoma, in only 4 or 5 of which the lesions were present at birth and none were located on the extremities. In a twenty-one year review of cases of fibrosarcoma at the Mayo Clinic3 only 1 case of congenital tumor was listed. More recently, Wells4 published a comprehensive review of the literature, in which 250 cases of congenital neoplasms are recorded. Of 95 cases reported as sarcoma, in 20 the tumors arose in the extremities. Other authors5 have reported single cases of congenital sarcoma in their series. It seems doubtful that there are more
CHAMBERLAIN JW, LAWRENCE KB. CONGENITAL SARCOMA OF EXTREMITIES: REPORT OF TWO CASES. Am J Dis Child. 1941;62(4):793–800. doi:10.1001/archpedi.1941.02000160094010
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