AN UNEXPECTED number of requests for reprints of a recent paper on arachnodactyly (Gray1) reveals a sufficiently active interest in anomalies of the fingers to warrant reporting a patient with another rare variety of such an anomaly.
About half a century ago (1894) a case of congenital spoon-shaped hands, due to fusion of fingers, combined with peaked skull, was first reported by Wheaton.2 The name was given to this condition by Apert3 (1906). His clinical note was superficial, as indeed were most of the subsequent case histories in the rather scanty literature. The memoir of real authority is that by Park and Powers4 (1920). Only 5 cases have appeared in the literature in this country, according to Sirkin,5 while the total number of authenticated cases is about 80, according to Cohn.6
REPORT OF A CASE
This baby boy was born Sept. 24, 1944, of
GRAY H, DICKEY LB. ACROCEPHALOSYNDACTYLY. Am J Dis Child. 1947;74(2):213–217. doi:10.1001/archpedi.1947.02030010221007
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