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Case Reports
May 1948

CUTIS ELASTICA: (Dermatorrhexis, Ehlers-Danlos Syndrome)

Author Affiliations

From the Department of Pediatrics, the Fargo Clinic and the North Dakota Children's Program.

Am J Dis Child. 1948;75(5):702-711. doi:10.1001/archpedi.1948.02030020719006

EHLERS1 and Danlos2 are responsible for recognizing and describing this syndrome in its entirety, although the condition is said to have been described as long ago as the time of Hippocrates.3 Ronchese4 reported 3 cases in 1936, and found 27 other typical cases in the literature. Tobias5 and Coe and Silvers6 have also given excellent reports of cases and reviews of the literature.

The clinical features of cutis elastica are (1) hyperelastic skin, which can be stretched easily for from 2 to 10 inches (5 to 25 cm.) above the surrounding skin; (2) a tendency of the skin to split easily on slight trauma; (3) usually papyraceous scars resulting from these lacerations which occur more commonly on the knees and elbows; (4) subcutaneous nodules, hematomas and pseudotumors forming in the tissues as an after-effect of trauma, and (5) articular overrelaxation in almost every case.

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