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June 1964

Double Outlet Right Ventricle With Pulmonic Stenosis

Author Affiliations

John Lintermans, MD, Department of Pediatrics, University of Washington School of Medicine, Seattle, Wash 98105.; Fellow in Pediatric Cardiology (Dr. Lintermans), Instructor of Pediatrics (Dr. Baum), and Associate Professor of Pediatrics (Dr. Guntheroth).

Am J Dis Child. 1964;107(6):632-635. doi:10.1001/archpedi.1964.02080060634014

Introduction  Double outlet right ventricle is a congenital cardiovascular anomaly in which both great arteries arise from the right ventricle, and the left ventricle is emptied through a ventricular septal defect.1-3 Pulmonic stenosis may occur in association.3-5The electrocardiographic findings in reported cases of double outlet right ventricle with pulmonic stenosis have been consistently those of right ventricular hypertrophy.4,6 Although electrocardiographic demonstration of left ventricular hypertrophy is found with this abnormality,7,8 to our knowledge it has always been reported to occur combined with right ventricular hypertrophy. The patient to be described is one with double outlet right ventricle and pulmonic stenosis, whose electrocardiogram was found to be consistent with isolated left ventricular hypertrophy.

Report of a Case  The baby was a 2-month-old male infant referred to the University Hospital because of increasing cyanosis and respiratory distress. Hypoxic spells had been occurring for one week prior to