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June 1965

Polyostotic Fibrous Dysplasia With Cutaneous Pigmentation: A Case in a Negro Male

Author Affiliations

From the Department of Pediatrics, Boston University School of Medicine and the Pediatric Service, Boston City Hospital. Junior Assistant Resident, Pediatric Service, Boston City Hospital, presently Senior Resident, Boston Floating Hospital (Dr. Caplan) and Assistant in Pediatrics, Boston University School of Medicine and Clinical Associate in Pediatrics, Boston City Hospital (Dr. Feingold).

Am J Dis Child. 1965;109(6):575-578. doi:10.1001/archpedi.1965.02090020577015

Introduction  FIBROUS dysplasia may be manifested by involvement of only one bone (monostotic), more than one (polyostotic), or by McCune-Albright syndrome. The original descriptions of McCune-Albright syndrome in this country consisted of café au lait spots, polyostotic fibrous dysplasia, and sexual precocity.1-3 There are a number of good reviews describing the clinical, radiological, and pathological aspects of this syndrome to which the reader is referred.1-8 In order to make this diagnosis, the classical triad should be present although some investigators5,6 do not consider sexual precocity to be necessary. Lichtenstein,9 in 1938 and again in 1942 in collaboration with Jaffe,10 stressed the pathological aspects of the bony abnormalities of the disease and termed the true nature of these as a fibrous dysplasia.A 6-year-old Negro boy was admitted to the Pediatric Service of the Boston City Hospital, presenting with polyostotic fibrous dysplasia and café au lait

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