Only two patients with truncus arteriosus associated with complete interruption of the aortic arch have been reported who survived infancy. A third child, not reported, has had surgical correction of these cardiac anomalies. All other reports of this combination of cardiac anomalies have dealt with patients who died in early infancy at a median age of 7 days. Because the condition is rare and because a corrective surgical procedure is available, a fourth child surviving infancy is reported.