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April 1973

Radiological Case of the Month

Author Affiliations

Los Angeles; La Mesa, Calif
From the Childrens Hospital of Los Angeles.

Am J Dis Child. 1973;125(4):539-540. doi:10.1001/archpedi.1973.04160040049010

Clinical History.  —This newborn girl was a product of a normal gestation and uncomplicated delivery. A repair of an omphalocele was done one hour after birth. Postoperatively there was mild respiratory distress and chest roentgenograms were obtained (Fig 1 and 2).Figures 1 and 2 show loops of bowel in the mediastinal area that appear to enter the mediastinum anteriorly. Surgical exploration through the omphalocele repair incision showed that the major portion of the incompletely rotated midgut had herniated into the pericardial cavity through a 3 X 31/2 cm anterior diaphragmatic defect. No cardiac or sternal abnormalities were noted. At the age of 1 year an innocent sounding cardiac murmur appeared. Otherwise, no further abnormalities have been found.In 1958, Cantrell et al1 described a syndrome of midline congenital defect characterized by absence of the lower sternum, diastasis recti with lateral insertion of the rectus muscles on