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May 1978

Association of Prune Belly Syndrome and Gastroschisis

Author Affiliations

Pritzker School of Medicine of The University of Chicago Department of Pediatrics 950 E 59th St Chicago, IL 60637

Am J Dis Child. 1978;132(5):526-527. doi:10.1001/archpedi.1978.02120300086019

Prune belly and gastroschisis are syndromes that have been well described in the literature. Prune belly or the "triad syndrome" is composed of cryptorchidism, deficiency of the abdominal wall, musculature, and urinary tract abnormalities.1 -4 Gastroschisis is a congenital full-thickness cleft in the abdominal wall, usually to the right of a normally inserting umbilical cord, and evisceration through the defect with no overlying membrane.5 -8 There have been more than 200 cases of prune belly and greater than 120 cases of gastroschisis reported in the literature, but the two syndromes have not, to our knowledge, been described together in the same patient. This report describes a patient with both prune belly syndrome and gastroschisis.

Report of a Case.—This infant was delivered from a gravida 9, para 7, 37-year-old woman on June 23, 1976 in Chicago Osteopathic Hospital. Excessive maternal alcohol consumption was the only complication of pregnancy.

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