Cinical History.—A newborn infant boy had respiratory distress that began immediately after birth.
Physical Examination.—He weighed 1,910 g, was tachypneic, with intercostal retractions and grunting, and had a slightly scaphoid abdomen. Combined chest and abdominal roentgenograms were obtained (Fig 1 and 2).
Denouement and Discussion
Split Notochord Syndrome
The vertebral anomalies of anterior and posterior spina bifida are often accompanied by a characteristic complex of visceral and neural abnormalities. One of the embryologic explanations for this combination of anterior and posterior spina bifida is the "split notochord" theory. This theory proposes that a primitive node cell rest persiiists in the midline, producing a notochordal cleft that causes the vertebral centra to be laid down in independent halves.1The most common visceral anomalies present in infants and children with the split notochord syndrome are mediastinal cysts of foregut origin (neurenteric cysts) and enteric duplications, most of which arise from the small
Young LW, Crowe JE, Sumner TE. Radiological Case of the Month. Am J Dis Child. 1978;132(8):813–814. doi:10.1001/archpedi.1978.02120330085019
Customize your JAMA Network experience by selecting one or more topics from the list below.
Create a personal account or sign in to: