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This monograph is 16th in the series Major Problems in Clinical Pediatrics. It lives up to the excellent reputation of the series by presenting the personal approach to muscle disorders of Victor Dubowitz, MD, who is internationally known and respected for his expertise in this area. The presentation is systematic, well written, and profusely illustrated, as well as authoritative. The confusing nomenclature of the ultrastructurally designated congenital myopathies is well handled, though one comes away with the notion that separation of this group of nonprogressive or very slowly progressive disorders is artificial at this level, and perhaps a fresh start with less emphasis on ultrastructure is the way of the future.
In addition to a workman-like presentation of the expected subjects of dystrophy, disorder of the lower motor neurons, myasthenia gravis, and the inflammatory myopathies, the author deals effectively with the somewhat newer and therapeutically important issues, such as