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February 1982

FG Syndrome-Reply

Author Affiliations

Children's Medical Center Tulsa, OK 74135

Am J Dis Child. 1982;136(2):177. doi:10.1001/archpedi.1982.03970380088028

In Reply.—Dr Zorn's comments are appreciated. However, there are many differences between the patients I and my colleagues studied and those with the FG syndrome.1,2 The patients with the FG syndrome commonly have severe mental retardation, whereas two of our patients showed only mild developmental delay. The oldest patient (case 3 in our report) with moderate mental retardation was not seen by us; therefore, this information about his mental abilities is anecdotal at best. The craniofacial features of our patients are also completely different than those with the FG syndrome. The patients we studied have trigonocephaly resulting in a narrow forehead with small anterior fontanel and hypotelorism, whereas patients with FG syndrome have large, open fontanels during infancy, with a high, broad forehead and hypertelorism. Craniosynostosis, in fact, is not a common finding in patients with the FG syndrome because, to the best of my knowledge, it was