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March 1988

Picture of the Month

Author Affiliations

Contributed from the Department of Pediatrics, Central Hospital, Helsingborg, Sweden.

Am J Dis Child. 1988;142(3):305-306. doi:10.1001/archpedi.1988.02150030079025

Denouement and Discussion 

Cutis Verticis Gyrata  Cutis verticis gyrata is characterized by convoluted furrows or folds of the scalp 1 to 2 cm thick. The furrows usually follow an anteroposterior course, but transverse folds are also present, especially in the occiput. The number of folds varies from two to approximately ten or 12. Hair is usually sparse in the areas of the folds. Mental retardation is frequently present, and other associated findings include microcephaly, seizures, and eye and brain abnormalities.There are primary and secondary forms of cutis verticis gyrata. The primary form is frequently inherited, and its manifestations are present at birth. The secondary form is associated with chronic inflammatory diseases, endocrine disorders, tumors, nevi, acromegaly, and pachydermoperiostos (Touraine-Solente-Golé syndrome).Patients should undergo magnetic resonance imaging or computed tomographic scan examinations to determine the presence and extent of any structural brain abnormalities. In patients with the secondary form, appropriate

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