A 7-year-old boy was admitted with a 1-month history of diminishing lower extremity strength and progressive loss of bowel and bladder control. He had been hospitalized 2 months earlier with similar symptoms. At that time, a benign paraspinous angiolipomatous tumor producing extradural spinal cord compression was diagnosed and successfully treated with angiographic embolization followed by decompressive laminectomy. Physical examination on admission revealed a frail, thin boy with a large subcutaneous mass involving the left chest wall and extending from the left nipple to the left axilla. Multiple smaller subcutaneous masses were also present on both arms and legs. Areas of increased skin pigmentation were scattered over his body, and a patch of roughened scalelike skin was present on his neck. Fixed deformities of the feet and ankles were present. Lower extremity strength was diminished. A chest roentgenogram (Fig 1), computed tomogram of the chest (Fig 2), magnetic resonance image of
Mitchell CS, Wood BP. Radiological Case of the Month. Am J Dis Child. 1993;147(12):1335–1336. doi:10.1001/archpedi.1993.02160360077023
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