THIS NEWBORN was referred for evaluation of a right nasal mass, apparent at birth. Mild respiratory distress was present (Figure 1). A magnetic resonance image (Figure 2) and a computed tomogram with intrathecal omnipaque (Figure 3) were obtained to evaluate the mass.
Denouement and Discussion
Nasal gliomas are rare, isolated, congenital lesions that are believed to be secondary to anterior displacement of nonneoplastic neuroglial tissue within or about the nose. The gliomas are usually noticed in infancy, but they may become apparent later in life. They present clinically as a nasal mass or fullness, producing some degree of nasal obstruction. Sixty percent of the tumors are extranasal, 30% are intranasal, and 10% are mixed (intranasal and extranasal).1 There is a slight predilection for males. They appear to be nonhereditary.
The nasal skin overlying extranasal gliomas is often normal. Occasionally, telangiectasia or a violaceous discoloration may
Derkay CS, Tunnessen WW. Pictures of the MonthCase 1. Arch Pediatr Adolesc Med. 1994;148(9):953–954. doi:10.1001/archpedi.1994.02170090067011
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