AMONG the recognized tumors of the esophagus, hemangioendotheliomas or lymphangioendotheliomas are extremely rare. We have been able to find only four cases reported. Three of these are to be found in the Italian literature, and one is in the American literature.
Frattin1 in 1903 described a case of primary lymphangioendothelioma in the cervical portion of the esophagus originating in a diverticulum about 2 cm. below the cricoid cartilage. In 1910 Carrara2 published a case of hemangioendothelioma of the esophagus that was discovered at autopsy. Macroscopically, this tumor resembled a carcinoma. Microscopically, however, many small neoplastic cells assuming both a cuboid and an oval shape were seen. The intimate grouping of these cells around vessels gave the impression that they were derived from the cells of the blood vessel walls, and hence the tumor was reported as a primary perivascular hemangioendothelioma of the esophagus.
In 1930 Mencarelli3 reported
PALANKER HK, CONSTANTINE AB, PAINE JR. SUCCESSFUL RESECTION OF AN ANGIOENDOTHELIOMA OF THE CERVICAL ESOPHAGUSCase Report and Review of the Literature. AMA Arch Surg. 1951;62(5):627–633. doi:10.1001/archsurg.1951.01250030637003
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