JAUNDICE due to common duct stones in association with congenital absence of the gall bladder is an extremely rare condition, since agenesis of the gall bladder itself is a rare anomaly. In 1945 Dixon and Lichtman1 reviewed 50 cases reported previously and added 10 cases studied at the Mayo Clinic. Stones were present in 27% of the cases. In 1947 Latimer, Mendez, and Hage2 collected 71 cases from the literature and added 3 cases of their own. In this series of 34 cases operated on, stones were found in 11. Villareal3 in 1948 reviewed 60 cases reported since 1900, and stones were found in the common duct or hepatic duct in 18 of 37 cases. The incidence of congenital absence of the gall bladder has been reported as being approximately 0.065%, on the basis of data obtained from autopsy material and clinical reports.
Embryologically, the anlage of
POLIVY C, SACHS JJ. CHOLEDOCHOLITHIASIS WITH CONGENITAL ABSENCE OF GALL BLADDER. AMA Arch Surg. 1954;68(5):720–722. doi:10.1001/archsurg.1954.01260050722020
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